OBJECTIVE: Patients with cleidocranial dysplasia often express concerns related to their perception of an undesirable esthetic appearance of their forehead and skull because of a combination of the persistence of metopic suture defects and frontal bossing. This case series reviews the use of a cranioplasty technique that has been developed to address such concerns. STUDY DESIGN: A series of 7 adult patients with cleidocranial dysplasia were treated using a cranioplasty technique to correct visible metopic suture defects in the forehead region. The patients were 4 males and 3 females with a mean age of 29.0 years. All 7 patients underwent identical cranioplasty procedures. RESULTS: The metopic suture cranial defects were found to range in size from 0.6 to 2.4 cm in diameter and were present as full-thickness osseous defects in 4 of the 7 patients. All postoperative complications resolved spontaneously. Inpatient admission times ranged from 1 to 3 days. Follow-up ranged from 9 to 48 months with satisfactory subjective esthetic outcomes. The patients were content in all cases. CONCLUSION: This cranioplasty procedure successfully addresses the specific esthetic concerns of a rare and unique group of individuals. The procedure can be offered to cleidocranial dysplasia patients as part of their overall comprehensive craniomaxillofacial management.
OBJECTIVE:Patients with cleidocranial dysplasia often express concerns related to their perception of an undesirable esthetic appearance of their forehead and skull because of a combination of the persistence of metopic suture defects and frontal bossing. This case series reviews the use of a cranioplasty technique that has been developed to address such concerns. STUDY DESIGN: A series of 7 adult patients with cleidocranial dysplasia were treated using a cranioplasty technique to correct visible metopic suture defects in the forehead region. The patients were 4 males and 3 females with a mean age of 29.0 years. All 7 patients underwent identical cranioplasty procedures. RESULTS: The metopic suture cranial defects were found to range in size from 0.6 to 2.4 cm in diameter and were present as full-thickness osseous defects in 4 of the 7 patients. All postoperative complications resolved spontaneously. Inpatient admission times ranged from 1 to 3 days. Follow-up ranged from 9 to 48 months with satisfactory subjective esthetic outcomes. The patients were content in all cases. CONCLUSION: This cranioplasty procedure successfully addresses the specific esthetic concerns of a rare and unique group of individuals. The procedure can be offered to cleidocranial dysplasiapatients as part of their overall comprehensive craniomaxillofacial management.
Authors: Olli-Pekka Lappalainen; Sakari S Karhula; Marianne Haapea; Sami Kauppinen; Mikko Finnilä; Simo Saarakkala; Willy Serlo; George K Sándor Journal: J Oral Maxillofac Res Date: 2016-06-30