Literature DB >> 16735769

Mucopolysaccharidosis IIIB, cerebral vasculopathy and recurrent subdural hematoma.

Mustafa Aydin1, Saadet Akarsu, Nimet Kabakus, Nusret Akpolat.   

Abstract

Mucopolysaccharidoses are characterized by involvement of multiple organs, including blood vessels. We present a case of mucopolysaccharidosis IIIB admitted with recurrent subdural hematoma; further evaluation and dural biopsy revealed an association with cerebral vasculopathy.

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Year:  2006        PMID: 16735769

Source DB:  PubMed          Journal:  Indian Pediatr        ISSN: 0019-6061            Impact factor:   1.411


  6 in total

Review 1.  Brain and spinal MR imaging findings in mucopolysaccharidoses: a review.

Authors:  D I Zafeiriou; S P Batzios
Journal:  AJNR Am J Neuroradiol       Date:  2012-07-12       Impact factor: 3.825

2.  Perioperative medullary complications in spinal and extra-spinal surgery in mucopolysaccharidosis: a case series of three patients.

Authors:  N Pauchard; C Garin; J L Jouve; P Lascombes; P Journeau
Journal:  JIMD Rep       Date:  2014-07-20

3.  Mucopolysaccharidosis IIIB (Sanfilippo syndrome B) in a commercial emu (Dromaius novaehollandiae) flock.

Authors:  Seiche C Genger; Keijiro Mizukami; Michael P Martin; Jeffrey R Applegate; H John Barnes; Urs Giger
Journal:  Avian Pathol       Date:  2017-10-10       Impact factor: 3.378

Review 4.  Hydrocephalus and mucopolysaccharidoses: what do we know and what do we not know?

Authors:  Amauri Dalla Corte; Carolina F M de Souza; Maurício Anés; Roberto Giugliani
Journal:  Childs Nerv Syst       Date:  2017-06-07       Impact factor: 1.475

5.  Chronic subdural hematoma associated with mucopolysaccharidosis type III B (Sanfilippo's syndrome B).

Authors:  Toshinari Kawasaki; Masashi Kitagawa; Keita Suzuki; Takafumi Wataya
Journal:  Childs Nerv Syst       Date:  2016-03-07       Impact factor: 1.475

6.  Posterior fossa horns; a new calvarial finding of mucopolysaccharidoses with well-known cranial MRI features.

Authors:  Çağri Damar; Betül Emine Derinkuyu; Muazzez Asburçe Bike Olgaç Kiliçkaya; Mehmet Öztürk; Çiğdem Öztunali; Ayşe Gül Alimli; Öznur Leman Boyunaga; Murat Uçar; Fatih Süheyl Ezgü; Leyla Tümer; Alp Özgün Börcek; Ahmet Siğirci
Journal:  Turk J Med Sci       Date:  2020-02-03       Impact factor: 0.973

  6 in total

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