Literature DB >> 15463956

Animal models of cystic fibrosis.

Bob J Scholte1, Donald J Davidson, Martina Wilke, Hugo R De Jonge.   

Abstract

Animal models of cystic fibrosis, in particular several different mutant mouse strains obtained by homologous recombination, have contributed considerably to our understanding of CF pathology. In this review, we describe and compare the main phenotypic features of these models. Recent and possible future developments in this field are discussed.

Entities:  

Mesh：

Year:  2004        PMID： 15463956     DOI： 10.1016/j.jcf.2004.05.039

Source DB:  PubMed          Journal:  J Cyst Fibros        ISSN： 1569-1993            Impact factor:   5.482


  29 in total

1.  Comparative biology of rAAV transduction in ferret, pig and human airway epithelia.

Authors:  X Liu; M Luo; C Guo; Z Yan; Y Wang; J F Engelhardt
Journal:  Gene Ther       Date:  2007-08-30       Impact factor: 5.250

2.  Regulation of hepatic sulfotransferase (SULT) 1E1 expression and effects on estrogenic activity in cystic fibrosis (CF).

Authors:  Charles N Falany; Dongning He; Li Li; Josie L Falany; Teresa W Wilborn; Thomas A Kocarek; Melissa Runge-Morris
Journal:  J Steroid Biochem Mol Biol       Date:  2009-03-03       Impact factor: 4.292

3.  Loss of CFTR affects biliary epithelium innate immunity and causes TLR4-NF-κB-mediated inflammatory response in mice.

Authors:  Romina Fiorotto; Roberto Scirpo; Michael Trauner; Luca Fabris; Rafaz Hoque; Carlo Spirli; Mario Strazzabosco
Journal:  Gastroenterology       Date:  2011-06-26       Impact factor: 22.682

4.  The porcine chloride channel calcium-activated family member pCLCA4a mirrors lung expression of the human hCLCA4.

Authors:  Stephanie Plog; Tanja Grötzsch; Nikolai Klymiuk; Ursula Kobalz; Achim D Gruber; Lars Mundhenk
Journal:  J Histochem Cytochem       Date:  2012-01       Impact factor: 2.479

Review 5.  Animal models for cystic fibrosis liver disease (CFLD).

Authors:  Romina Fiorotto; Mariangela Amenduni; Valeria Mariotti; Massimiliano Cadamuro; Luca Fabris; Carlo Spirli; Mario Strazzabosco
Journal:  Biochim Biophys Acta Mol Basis Dis       Date:  2018-07-30       Impact factor: 5.187

Review 6.  Barriers to inhaled gene therapy of obstructive lung diseases: A review.

Authors:  Namho Kim; Gregg A Duncan; Justin Hanes; Jung Soo Suk
Journal:  J Control Release       Date:  2016-05-16       Impact factor: 9.776

7.  Characterisation of electrogenic nutrient absorption in the Cftr TgH(neoim)Hgu mouse model.

Authors:  B Tóth; S Leonhard-Marek; H J Hedrich; G Breves
Journal:  J Comp Physiol B       Date:  2008-03-28       Impact factor: 2.200

8.  Genomic, tissue expression, and protein characterization of pCLCA1, a putative modulator of cystic fibrosis in the pig.

Authors:  Stephanie Plog; Lars Mundhenk; Nikolai Klymiuk; Achim D Gruber
Journal:  J Histochem Cytochem       Date:  2009-09-15       Impact factor: 2.479

9.  Transcription-dependent spatial arrangements of CFTR and conserved adjacent loci are not conserved in human and murine nuclei.

Authors:  Nicolas Sadoni; Bianca-Sabrina Targosz; Andreas Englmann; Stephanie Fesser; Jeannette Koch; Dirk Schindelhauer; Daniele Zink
Journal:  Chromosoma       Date:  2008-04-12       Impact factor: 4.316

Review 10.  Pancreatic pathophysiology in cystic fibrosis.

Authors:  Katherine N Gibson-Corley; David K Meyerholz; John F Engelhardt
Journal:  J Pathol       Date:  2015-10-01       Impact factor: 7.996
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