Literature DB >> 15354333

Molecular screening for diseases frequent in Ashkenazi Jews: lessons learned from more than 100,000 tests performed in a commercial laboratory.

Charles M Strom1, Beryl Crossley, Joy B Redman, Franklin Quan, Arlene Buller, Matthew J McGinniss, Weimin Sun.   

Abstract

PURPOSE: To determine the frequency of carriers of Ashkenazi Jewish (AJ) genetic diseases in the US population and compare these numbers with previously published frequencies reported in smaller more isolated cohorts.
METHODS: A database containing more than 100,000 genotyping assays was queried. Assays for 10 separate AJ genetic diseases where comparisons were made with published data.
RESULTS: As expected, we observed lower carrier frequencies in a general, US population than those reported in literature. In 2427 patients tested for a panel of 8 AJ diseases, 20 (1:121) were carriers of two diseases and 331 (1:7) were carriers of a single disease. Fifty-three of 7184 (1:306) individuals tested for Gaucher disease had 2 Gaucher Disease mutations indicating a potentially affected phenotype.
CONCLUSIONS: As the number of AJ diseases increases, progressively more individuals will be identified as carriers of at least one disease.

Entities:  

Mesh:

Year:  2004        PMID: 15354333     DOI: 10.1097/01.gim.0000127267.57526.d1

Source DB:  PubMed          Journal:  Genet Med        ISSN: 1098-3600            Impact factor:   8.822


  15 in total

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2.  Comprehensive arrayed primer extension array for the detection of 59 sequence variants in 15 conditions prevalent among the (Ashkenazi) Jewish population.

Authors:  Iris Schrijver; Maigi Külm; Phyllis I Gardner; Eugene P Pergament; Morris B Fiddler
Journal:  J Mol Diagn       Date:  2007-04       Impact factor: 5.568

3.  Human chitotriosidase polymorphisms G354R and A442V associated with reduced enzyme activity.

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9.  Rapid one-step carrier detection assay of mucolipidosis IV mutations in the Ashkenazi Jewish population.

Authors:  Feras M Hantash; Susan C Olson; Ben Anderson; Arlene Buller; Rebecca Chen; Beryl Crossly; Weimin Sun; Charles M Strom
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10.  Technical validation of a TM Biosciences Luminex-based multiplex assay for detecting the American College of Medical Genetics recommended cystic fibrosis mutation panel.

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Journal:  J Mol Diagn       Date:  2006-07       Impact factor: 5.568

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