Unicornuate uterus and unilateral ovarian agenesis associated with pelvic kidney.

In this report, we present a case of unilateral müllerian and ovarian agenesis associated with pelvic kidney. The patient was a 27-year-old woman who complained of an inability to conceive. We performed a hysterosalpingogram, hysteroscopy, laparoscopy, and an excretory urogram (IVP). At laparoscopy, we found an unicornuate uterus without a rudimentary horn. The right round ligament, fallopian tube, and ovary were present, but they were absent at the left side. Postoperative IVP revealed a pelvic kidney. Ultimately, her infertility was found to be due to a male factor: the abnormal semen of her partner. The couple was referred to our in vitro fertilization (IVF) unit. Because of the close embryologic association between the genital and urinary tracts, evaluation of the urinary tract in any patient with a genital or gonadal anomaly is necessary.