Literature DB >> 11585674

Mouse models of cystic fibrosis.

D J Davidson1, M Rolfe.   

Abstract

The development of mouse models for cystic fibrosis has provided the opportunity to dissect disease pathogenesis, correlate genotype and phenotype, study disease-modifying genes and develop novel therapeutics. This review discusses the successes and the challenges encountered in characterizing and optimizing these models.

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Year:  2001        PMID: 11585674     DOI: 10.1016/s0168-9525(01)02452-0

Source DB:  PubMed          Journal:  Trends Genet        ISSN: 0168-9525            Impact factor:   11.639


  20 in total

1.  Low linoleic and high docosahexaenoic acids in a severe phenotype of transgenic cystic fibrosis mice.

Authors:  Birgitta Strandvik; Wanda K O Neal; Mohamed A Ali; Ulf Hammar
Journal:  Exp Biol Med (Maywood)       Date:  2018-03

2.  The porcine chloride channel calcium-activated family member pCLCA4a mirrors lung expression of the human hCLCA4.

Authors:  Stephanie Plog; Tanja Grötzsch; Nikolai Klymiuk; Ursula Kobalz; Achim D Gruber; Lars Mundhenk
Journal:  J Histochem Cytochem       Date:  2012-01       Impact factor: 2.479

3.  Listeria monocytogenes exploits cystic fibrosis transmembrane conductance regulator (CFTR) to escape the phagosome.

Authors:  Andrea L Radtke; Kelsi L Anderson; Michael J Davis; Matthew J DiMagno; Joel A Swanson; Mary X O'Riordan
Journal:  Proc Natl Acad Sci U S A       Date:  2011-01-10       Impact factor: 11.205

4.  Species-specific differences in mouse and human airway epithelial biology of recombinant adeno-associated virus transduction.

Authors:  Xiaoming Liu; Ziying Yan; Meihui Luo; John F Engelhardt
Journal:  Am J Respir Cell Mol Biol       Date:  2005-09-29       Impact factor: 6.914

5.  Differential persistence among genomovars of the Burkholderia cepacia complex in a murine model of pulmonary infection.

Authors:  Karen K Chu; Donald J Davidson; T Keith Halsey; Jacqueline W Chung; David P Speert
Journal:  Infect Immun       Date:  2002-05       Impact factor: 3.441

6.  Comparative biology of cystic fibrosis animal models.

Authors:  John T Fisher; Yulong Zhang; John F Engelhardt
Journal:  Methods Mol Biol       Date:  2011

7.  The cystic fibrosis transmembrane conductance regulator (Cftr) modulates the timing of puberty in mice.

Authors:  R Jin; C A Hodges; M L Drumm; M R Palmert
Journal:  J Med Genet       Date:  2006-06       Impact factor: 6.318

Review 8.  Therapeutics based on stop codon readthrough.

Authors:  Kim M Keeling; Xiaojiao Xue; Gwen Gunn; David M Bedwell
Journal:  Annu Rev Genomics Hum Genet       Date:  2014-04-18       Impact factor: 8.929

Review 9.  The cystic fibrosis gene: a molecular genetic perspective.

Authors:  Lap-Chee Tsui; Ruslan Dorfman
Journal:  Cold Spring Harb Perspect Med       Date:  2013-02-01       Impact factor: 6.915

10.  Tissue and cellular expression patterns of porcine CFTR: similarities to and differences from human CFTR.

Authors:  Stephanie Plog; Lars Mundhenk; Melanie K Bothe; Nikolai Klymiuk; Achim D Gruber
Journal:  J Histochem Cytochem       Date:  2010-05-24       Impact factor: 2.479

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