Literature DB >> 9890072

Alpha 1-antitrypsin deficiency.

S Eriksson1, A N Elzouki.   

Abstract

Alpha 1-Antitrypsin deficiency (PiZ) is frequent in Caucasian populations. The predominant clinical correlates of this inborn error, i.e. chronic liver disease, emphysema, and vasculitic syndromes including their pathogenetic background are discussed in the present review.

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Year:  1998        PMID: 9890072     DOI: 10.1016/s0950-3528(98)90134-8

Source DB:  PubMed          Journal:  Baillieres Clin Gastroenterol        ISSN: 0950-3528


  2 in total

1.  Alpha 1-antitrypsin activity is markedly decreased in Wegener's granulomatosis.

Authors:  Ali Mota; Abbas Sahebghadam Lotfi; Ahmad-Reza Jamshidi; Saeed Najavand
Journal:  Rheumatol Int       Date:  2013-04-19       Impact factor: 2.631

2.  Evaluation of Alpha-1 Antitrypsin Levels and SERPINA1 Gene Polymorphisms in Sickle Cell Disease.

Authors:  Magda Oliveira Seixas Carvalho; André Luís Carvalho Santos Souza; Mauricio Batista Carvalho; Ana Paula Almeida Souza Pacheco; Larissa Carneiro Rocha; Valma Maria Lopes do Nascimento; Camylla Vilas Boas Figueiredo; Caroline Conceição Guarda; Rayra Pereira Santiago; Adekunle Adekile; Marilda de Souza Goncalves
Journal:  Front Immunol       Date:  2017-11-06       Impact factor: 7.561

  2 in total

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