Literature DB >> 987160

Control of pyruvate and beta-hydroxybutyrate utilization in rat brain mitochondria and its relevance to phenylketonuria and maple syrup urine disease.

J M Land, J Mowbray, J B Clark.   

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Year:  1976        PMID： 987160     DOI： 10.1111/j.1471-4159.1976.tb04458.x

Source DB:  PubMed          Journal:  J Neurochem        ISSN： 0022-3042            Impact factor:   5.372


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  24 in total

1.  Creatine and antioxidant treatment prevent the inhibition of creatine kinase activity and the morphological alterations of C6 glioma cells induced by the branched-chain alpha-keto acids accumulating in maple syrup urine disease.

Authors:  Cláudia Funchal; Patrícia Fernanda Schuck; André Quincozes Dos Santos; Maria Caroline Jacques-Silva; Carmem Gottfried; Regina Pessoa-Pureur; Moacir Wajner
Journal:  Cell Mol Neurobiol       Date:  2006-02       Impact factor: 5.046

2.  Effect of alpha-ketoisocaproate and leucine on the in vivo oxidation of glutamate and glutamine in the rat brain.

Authors:  H R Zielke; Y Huang; P J Baab; R M Collins; C L Zielke; J T Tildon
Journal:  Neurochem Res       Date:  1997-09       Impact factor: 3.996

3.  Acute Administration of Branched-Chain Amino Acids Increases the Pro-BDNF/Total-BDNF Ratio in the Rat Brain.

Authors:  Giselli Scaini; Meline O S Morais; Camila B Furlanetto; Luiza W Kist; Talita C B Pereira; Patrícia F Schuck; Gustavo C Ferreira; Matheus A B Pasquali; Daniel P Gelain; José Cláudio F Moreira; Maurício R Bogo; Emilio L Streck
Journal:  Neurochem Res       Date:  2015-02-14       Impact factor: 3.996

4.  Morphological alterations and cell death provoked by the branched-chain alpha-amino acids accumulating in maple syrup urine disease in astrocytes from rat cerebral cortex.

Authors:  Cláudia Funchal; Carmem Gottfried; Lúcia Maria Vieira de Almeida; André Quincozes dos Santos; Moacir Wajner; Regina Pessoa-Pureur
Journal:  Cell Mol Neurobiol       Date:  2005-08       Impact factor: 5.046

5.  alpha-keto acids accumulating in maple syrup urine disease stimulate lipid peroxidation and reduce antioxidant defences in cerebral cortex from young rats.

Authors:  Raquel Bridi; César A Braun; Giovanni K Zorzi; Clóvis M D Wannmacher; Moacir Wajner; Eduardo G Lissi; Carlos Severo Dutra-Filho
Journal:  Metab Brain Dis       Date:  2005-06       Impact factor: 3.584

6.  Branched chain amino acids induce apoptosis in neural cells without mitochondrial membrane depolarization or cytochrome c release: implications for neurological impairment associated with maple syrup urine disease.

Authors:  P Jouvet; P Rustin; D L Taylor; J M Pocock; U Felderhoff-Mueser; N D Mazarakis; C Sarraf; U Joashi; M Kozma; K Greenwood; A D Edwards; H Mehmet
Journal:  Mol Biol Cell       Date:  2000-05       Impact factor: 4.138

7.  Behavioral responses in rats submitted to chronic administration of branched-chain amino acids.

Authors:  Giselli Scaini; Gabriela C Jeremias; Camila B Furlanetto; Diogo Dominguini; Clarissa M Comim; João Quevedo; Patrícia F Schuck; Gustavo C Ferreira; Emilio L Streck
Journal:  JIMD Rep       Date:  2013-11-09

8.  Biochemical, Metabolic, and Behavioral Characteristics of Immature Chronic Hyperphenylalanemic Rats.

Authors:  Gerald A Dienel; Nancy F Cruz
Journal:  Neurochem Res       Date:  2015-07-30       Impact factor: 3.996

9.  Reduction of glutamate uptake into cerebral cortex of developing rats by the branched-chain alpha-keto acids accumulating in maple syrup urine disease.

Authors:  Cláudia Funchal; Aline Meyer Rosa; Moacir Wajner; Susana Wofchuk; Regina Pessoa Pureur
Journal:  Neurochem Res       Date:  2004-04       Impact factor: 3.996

Review 10.  The biochemical basis of mitochondrial diseases.

Authors:  H R Scholte
Journal:  J Bioenerg Biomembr       Date:  1988-04       Impact factor: 2.945
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