Literature DB >> 9659504

Failure to control the airway in a patient with Hunter's syndrome.

L Gaitini1, M Fradis, S Vaida, G Collins, M Croitoru, M Somri, Z Borochovitz, A Golz.   

Abstract

Hunter's syndrome is due to recessively inherited mucopolysaccharide storage diseases. The anaesthetic complications in this syndrome are related to the organs involved in the disease, but pertain especially to upper airway obstruction problems. We report a patient with Hunter's syndrome who, while under general anaesthesia for a simple procedure (the introduction of bilateral grommets), suffered a fatal outcome.

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Year:  1998        PMID： 9659504     DOI： 10.1017/s0022215100140526

Source DB:  PubMed          Journal:  J Laryngol Otol        ISSN： 0022-2151            Impact factor:   1.469


  3 in total

1.  Management of Life-Threatening Tracheal Stenosis and Tracheomalacia in Patients with Mucopolysaccharidoses.

Authors:  Christoph Kampmann; Christiane M Wiethoff; Ralf G Huth; Gundula Staatz; Eugen Mengel; Michael Beck; Stefan Gehring; Torsten Mewes; Tariq Abu-Tair
Journal:  JIMD Rep       Date:  2016-07-22

Review 2.  Mucopolysaccharidosis type II (Hunter syndrome): a clinical review and recommendations for treatment in the era of enzyme replacement therapy.

Authors:  J Edmond Wraith; Maurizio Scarpa; Michael Beck; Olaf A Bodamer; Linda De Meirleir; Nathalie Guffon; Allan Meldgaard Lund; Gunilla Malm; Ans T Van der Ploeg; Jiri Zeman
Journal:  Eur J Pediatr       Date:  2007-11-23       Impact factor: 3.183

3.  Presentation and Treatments for Mucopolysaccharidosis Type II (MPS II; Hunter Syndrome).

Authors:  Molly Stapleton; Francyne Kubaski; Robert W Mason; Hiromasa Yabe; Yasuyuki Suzuki; Kenji E Orii; Tadao Orii; Shunji Tomatsu
Journal:  Expert Opin Orphan Drugs       Date:  2017-03-08       Impact factor: 0.694
  3 in total

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