Literature DB >> 9627601

Treatment of hemoglobin Bart's hydrops with bone marrow transplantation.

K W Chik1, M M Shing, C K Li, T F Leung, K S Tsang, H L Yuen, S B Cheng, P M Yuen.   

Abstract

A 21-month-old girl with hemoglobin Bart's hydrops received bone marrow transplantation (BMT) from a matched sibling. No major BMT-related complications developed. Hemoglobin levels remained greater than 10 gm/dl for 20 months without blood transfusion support despite the presence of residual host hemopoietic cells from 2 months after BMT. We suggest consideration of this therapeutic option for surviving patients.

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Year:  1998        PMID: 9627601     DOI: 10.1016/s0022-3476(98)70406-8

Source DB:  PubMed          Journal:  J Pediatr        ISSN: 0022-3476            Impact factor:   4.406


  9 in total

Review 1.  Haemolytic disease of the newborn.

Authors:  Neil A Murray; Irene A G Roberts
Journal:  Arch Dis Child Fetal Neonatal Ed       Date:  2007-03       Impact factor: 5.747

2.  Normal cognitive functioning in a patient with Hb Bart's hydrops successfully cured by hematopoietic SCT.

Authors:  B Pongtanakul; K Sanpakit; V Chongkolwatana; V Viprakasit
Journal:  Bone Marrow Transplant       Date:  2013-08-26       Impact factor: 5.483

Review 3.  An international registry of survivors with Hb Bart's hydrops fetalis syndrome.

Authors:  Duantida Songdej; Christian Babbs; Douglas R Higgs
Journal:  Blood       Date:  2017-01-05       Impact factor: 22.113

Review 4.  Hydrops fetalis caused by homozygous alpha-thalassemia and Rh antigen alloimmunization: report of a survivor and literature review.

Authors:  Divya-Devi Joshi; H James Nickerson; Michael J McManus
Journal:  Clin Med Res       Date:  2004-11

Review 5.  Advances in the management of α-thalassemia major: reasons to be optimistic.

Authors:  Paulina Horvei; Tippi MacKenzie; Sandhya Kharbanda
Journal:  Hematology Am Soc Hematol Educ Program       Date:  2021-12-10

6.  Fetal gene therapy of alpha-thalassemia in a mouse model.

Authors:  Xiao-Dong Han; Chin Lin; Judy Chang; Michel Sadelain; Y W Kan
Journal:  Proc Natl Acad Sci U S A       Date:  2007-05-11       Impact factor: 11.205

7.  Successful matched unrelated donor stem cell transplant in Hemoglobin Bart's disease.

Authors:  M Y Elsaid; C M Capitini; C A Diamond; M Porte; M Otto; K B DeSantes
Journal:  Bone Marrow Transplant       Date:  2016-06-13       Impact factor: 5.483

8.  Association of Tissue-Specific DNA Methylation Alterations with α-Thalassemia Southeast Asian Deletion.

Authors:  Tanapat Pangeson; Phanchana Sanguansermsri; Torpong Sanguansermsri; Teerapat Seeratanachot; Narutchala Suwanakhon; Metawee Srikummool; Worasak Kaewkong; Khwanruedee Mahingsa
Journal:  Genet Epigenet       Date:  2017-11-15

9.  Forager and farmer evolutionary adaptations to malaria evidenced by 7000 years of thalassemia in Southeast Asia.

Authors:  Melandri Vlok; Hallie R Buckley; Justyna J Miszkiewicz; Meg M Walker; Kate Domett; Anna Willis; Hiep H Trinh; Tran T Minh; Mai Huong T Nguyen; Lan Cuong Nguyen; Hirofumi Matsumura; Tianyi Wang; Huu T Nghia; Marc F Oxenham
Journal:  Sci Rep       Date:  2021-03-11       Impact factor: 4.379

  9 in total

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