Literature DB >> 9569265

Intestinal rotational abnormalities in polysplenia and asplenia syndromes.

M R Ditchfield1, J M Hutson.   

Abstract

OBJECTIVE: To review the anomalies of intestinal rotation occurring in association with asplenia (right isomerism) and polysplenia (left isomerism) syndromes.
MATERIALS AND METHODS: A retrospective study was performed of 27 children with asplenia (21) or polysplenia (6) identified from the cardiology and radiology databases from 1988 to 1996 and in whom an upper gastrointestinal barium study had been performed. The intestinal rotation was determined by reviewing the barium meal and could be divided into four groups: (1) normal rotation, (2) incomplete rotation or nonrotation, (3) reversed rotation and (4) reversed incomplete rotation or nonrotation. Surgical correlation was obtained at laparotomy in 17 patients.
RESULTS: Of the 27 children studied, 3 (11 %) had normal rotation; incomplete rotation or nonrotation occurred in 5 (19 %), and 2 in this group developed midgut volvulus; 5 (19 %) had reversed rotation; 14 (52 %) had reversed incomplete rotation or nonrotation.
CONCLUSION: Asplenia and polysplenia are frequently associated with intestinal malrotation, and a barium study is recommended in all of these children, as many will be at risk of midgut volvulus.

Entities:  

Mesh:

Year:  1998        PMID: 9569265     DOI: 10.1007/s002470050358

Source DB:  PubMed          Journal:  Pediatr Radiol        ISSN: 0301-0449


  16 in total

Review 1.  Disorders of intestinal rotation and fixation ("malrotation").

Authors:  Peter J Strouse
Journal:  Pediatr Radiol       Date:  2004-09-04

2.  Heterotaxy syndrome: is a prophylactic Ladd procedure necessary in asymptomatic patients?

Authors:  Charissa R Pockett; Bryan Dicken; Ivan M Rebeyka; David B Ross; Lindsay M Ryerson
Journal:  Pediatr Cardiol       Date:  2012-05-29       Impact factor: 1.655

3.  Adult midgut malrotation: multi-detector computed tomography (MDCT) findings of 14 cases.

Authors:  Bin Yang; Wen-Hui Chen; Xiao-Feng Zhang; Zhong-Rao Luo
Journal:  Jpn J Radiol       Date:  2013-03-09       Impact factor: 2.374

4.  Heterotaxy syndrome: defining contemporary disease trends.

Authors:  Terence W Prendiville; Leslie L Barton; William R Thompson; Doran L Fink; Kathryn W Holmes
Journal:  Pediatr Cardiol       Date:  2010-08-21       Impact factor: 1.655

Review 5.  Imaging of patients with congenital heart disease.

Authors:  Arno A W Roest; Albert de Roos
Journal:  Nat Rev Cardiol       Date:  2011-11-01       Impact factor: 32.419

6.  A case of unusual visceral heterotaxy syndrome with isolated levocardia.

Authors:  Dae Sun Jo; Sung Su Jung; Chan Uhng Joo
Journal:  Korean Circ J       Date:  2013-10-30       Impact factor: 3.243

7.  Deciphering normal and anomalous viscero-atrial situs on multidetector CT angiography.

Authors:  Niraj Nirmal Pandey; Mumun Sinha; Rengarajan Rajagopal; Arun Sharma; Sanjeev Kumar
Journal:  Br J Radiol       Date:  2019-07-10       Impact factor: 3.039

Review 8.  Somatostatin or octreotide as treatment options for chylothorax in young children: a systematic review.

Authors:  Charles C Roehr; Andreas Jung; Hans Proquitté; Oliver Blankenstein; Hannes Hammer; Kokila Lakhoo; Roland R Wauer
Journal:  Intensive Care Med       Date:  2006-03-11       Impact factor: 17.440

Review 9.  Polysplenia syndrome: a review of the relationship with viscero-atrial situs and the spectrum of extra-cardiac anomalies.

Authors:  Ahmed M Tawfik; Nihal M Batouty; Mona M Zaky; Mohamed A Eladalany; Ali H Elmokadem
Journal:  Surg Radiol Anat       Date:  2013-03-19       Impact factor: 1.246

10.  Heterotaxy and intestinal rotation anomalies: 20 years experience at a UK regional paediatric surgery centre.

Authors:  Paul S Cullis; Sotirios Siminas; Adeline Salim; Robert Johnson; Paul D Losty
Journal:  Pediatr Surg Int       Date:  2015-08-05       Impact factor: 1.827

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