Literature DB >> 9544222

Treatment of children with relapsed soft tissue sarcoma: report of the German CESS/CWS REZ 91 trial.

T Klingebiel1, U Pertl, C F Hess, H Jürgens, E Koscielniak, R Pötter, R van Heek-Romanowski, R Rossi, C Schött, H J Spaar, U Willnow, J Treuner.   

Abstract

BACKGROUND: The present study was performed to evaluate the possibilities of relapse treatment in patients heavily pretreated for a soft tissue sarcoma. PATIENTS AND METHODS: Prospective, multicenter study in 44 soft tissue sarcoma (STS) patients with first relapse. Primary diagnosis was embryonal rhabdomyosarcoma (RME) in 17 patients, alveolar rhabdomyosarcoma (RMA) in 13, primitive neuroectodermal tumor (PNET) in 6, and miscellaneous soft tissue sarcomas in 8 patients. Initial chemotherapy consisted of carboplatin/etoposide combination (150 mg/m2 each, days 1 to 4) followed by local therapy including surgical treatment and, whenever possible, radiotherapy.
RESULTS: In 11/17 patients without primary tumor resection, CR or PR was achieved following the initial two cycles of chemotherapy (61%). The probability of event-free survival (pEFS) for RME patients was 0.41 +/- 0.12 at 5 years, and 0.25 +/- 0.12 for RMA patients. But, in contrast no PNET patient or patient with another soft-tissue sarcoma achieved long-term remission. Additional local radiotherapy significantly (P = 0.002) improved pEFS (3-year estimates of 0.23 +/- 0.2 vs. 0.1 +/- 0.1 in patients without radiotherapy).
CONCLUSIONS: In patients with RME, relapse treatment employing a carboplatin/etoposide combination may induce a second remission in approximately 40% of patients. Surgical excision and additional local radiotherapy seem to be essential to maintain a stable remission. In patients with RMA or PNET, however, this treatment strategy is of no long-term benefit.

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Year:  1998        PMID: 9544222     DOI: 10.1002/(sici)1096-911x(199805)30:5<269::aid-mpo2>3.0.co;2-d

Source DB:  PubMed          Journal:  Med Pediatr Oncol        ISSN: 0098-1532


  10 in total

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Review 3.  Clinical aspects of alveolar rhabdomyosarcoma with translocation t(1;13)(p36;q14) and hypotetraploidy.

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5.  Soft tissue sarcoma in children: prognosis and management.

Authors:  Ewa Koscielniak; Mary Morgan; Jörn Treuner
Journal:  Paediatr Drugs       Date:  2002       Impact factor: 3.022

6.  Phase 1 study of an oxaliplatin and etoposide regimen in pediatric patients with recurrent solid tumors.

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7.  Preclinical Justification of pbi-shRNA EWS/FLI1 Lipoplex (LPX) Treatment for Ewing's Sarcoma.

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Review 8.  Management of Refractory Pediatric Sarcoma: Current Challenges and Future Prospects.

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9.  D,L-Methadone enhances the cytotoxic activity of standard chemotherapeutic agents on pediatric rhabdomyosarcoma.

Authors:  Cristian Urla; Irene Corteletti; Ann-Sophie Raible; Rupert Handgretinger; Jörg Fuchs; Steven W Warmann; Evi Schmid
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10.  Is there a role for salvage re-irradiation in pediatric patients with locoregional recurrent rhabdomyosarcoma? Clinical outcomes from a multi-institutional cohort.

Authors:  Daniel V Wakefield; Bree R Eaton; Austin P H Dove; Chih-Yang Hsu; Thomas E Merchant; Alberto Pappo; Andrew M Davidoff; Natia Esiashvili; Matthew J Krasin; John T Lucas
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  10 in total

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