BACKGROUND: The myelocystocele is a rare clinical entity, and there have only been six case reports concerning the cervical myelocystocele, including ours. METHODS: The case of a female neonate with cervical myelocystocele, who presented with respiratory distress beginning at birth is reported. RESULTS: Magnetic resonance (MR) imaging disclosed a cystic lesion surrounded by two layers of membrane, which were recognized to be the dural and arachnoid layer and the ependymal lining layer, respectively, during operation and on histopathologic examination. Hydromyelia at C2-C7 with Chiari II malformation was also observed. After a thorough repair and untethering surgery, the hydromyelia was diminished on a follow-up MR examination. The patient's respiratory status normalized several days postoperatively, and her growth and development were within normal limits at the 2-year follow-up. CONCLUSIONS: In cases of cervical myelocystocele with Chiari II malformation, untethering through intradural exploration to treat the tethered cord and outer decompression of the foramen magnum are needed. MR imaging is the best modality for preoperative determination of anatomic relationships.
BACKGROUND: The myelocystocele is a rare clinical entity, and there have only been six case reports concerning the cervical myelocystocele, including ours. METHODS: The case of a female neonate with cervical myelocystocele, who presented with respiratory distress beginning at birth is reported. RESULTS: Magnetic resonance (MR) imaging disclosed a cystic lesion surrounded by two layers of membrane, which were recognized to be the dural and arachnoid layer and the ependymal lining layer, respectively, during operation and on histopathologic examination. Hydromyelia at C2-C7 with Chiari II malformation was also observed. After a thorough repair and untethering surgery, the hydromyelia was diminished on a follow-up MR examination. The patient's respiratory status normalized several days postoperatively, and her growth and development were within normal limits at the 2-year follow-up. CONCLUSIONS: In cases of cervical myelocystocele with Chiari II malformation, untethering through intradural exploration to treat the tethered cord and outer decompression of the foramen magnum are needed. MR imaging is the best modality for preoperative determination of anatomic relationships.
Authors: J Francisco Salomão; Sérgio Cavalheiro; Hamilton Matushita; René D Leibinger; Antonio R Bellas; Elide Vanazzi; Luiz A M de Souza; Andréa G Nardi Journal: Childs Nerv Syst Date: 2005-06-04 Impact factor: 1.475
Authors: Waldo Sepulveda; Amy E Wong; Francisco Sepulveda; Juan L Alcalde; Juan C Devoto; Felipe Otayza Journal: Childs Nerv Syst Date: 2017-06-07 Impact factor: 1.475
Authors: Ramona Woitek; Anton Dvorak; Michael Weber; Rainer Seidl; Dieter Bettelheim; Veronika Schöpf; Gabriele Amann; Peter C Brugger; Julia Furtner; Ulrika Asenbaum; Daniela Prayer; Gregor Kasprian Journal: PLoS One Date: 2014-11-13 Impact factor: 3.240