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12 in total

Review 1. Evidence for both the nucleus and cytoplasm as subcellular sites of pathogenesis in Huntington's disease in cell culture and in transgenic mice expressing mutant huntingtin.

Authors: A S Hackam; J G Hodgson; R Singaraja; T Zhang; L Gan; C A Gutekunst; S M Hersch; M R Hayden
Journal: Philos Trans R Soc Lond B Biol Sci Date: 1999-06-29 Impact factor: 6.237

Review 2. The complex clinical and genetic classification of inherited ataxias. I. Dominant ataxias.

Authors: S Di Donato
Journal: Ital J Neurol Sci Date: 1998-12

3. Ataxin active site determination using spectral distribution of electron ion interaction potentials of amino acids.

Authors: E Pirogova; V Vojisavljevic; J L Hernández Cáceres; I Cosic
Journal: Med Biol Eng Comput Date: 2010-02-11 Impact factor: 2.602

Review 4. PGC-1α at the intersection of bioenergetics regulation and neuron function: from Huntington's disease to Parkinson's disease and beyond.

Authors: Taiji Tsunemi; Albert R La Spada
Journal: Prog Neurobiol Date: 2011-11-09 Impact factor: 11.685

5. Transglutaminase aggregates huntingtin into nonamyloidogenic polymers, and its enzymatic activity increases in Huntington's disease brain nuclei.

Authors: M V Karpuj; H Garren; H Slunt; D L Price; J Gusella; M W Becher; L Steinman
Journal: Proc Natl Acad Sci U S A Date: 1999-06-22 Impact factor: 11.205

Polyglutamines, nuclear inclusions and neurodegeneration.

Review 1. Evidence for both the nucleus and cytoplasm as subcellular sites of pathogenesis in Huntington's disease in cell culture and in transgenic mice expressing mutant huntingtin.

Review 2. The complex clinical and genetic classification of inherited ataxias. I. Dominant ataxias.

3. Ataxin active site determination using spectral distribution of electron ion interaction potentials of amino acids.

Review 4. PGC-1α at the intersection of bioenergetics regulation and neuron function: from Huntington's disease to Parkinson's disease and beyond.

5. Transglutaminase aggregates huntingtin into nonamyloidogenic polymers, and its enzymatic activity increases in Huntington's disease brain nuclei.

6. Characterization of intracellular aggregates using fluorescently-tagged polyglutamine-expanded androgen receptor.

7. Molecular clearance of ataxin-3 is regulated by a mammalian E4.

8. CAG repeats mimic CUG repeats in the misregulation of alternative splicing.

9. Recruitment and the role of nuclear localization in polyglutamine-mediated aggregation.

Review 10. UBE4B: a promising regulatory molecule in neuronal death and survival.