Literature DB >> 9266362

Nerve cell lesions caused by 3-hydroxyglutaric acid: a possible mechanism for neurodegeneration in glutaric acidaemia I.

B Flott-Rahmel1, C Falter, P Schluff, R Fingerhut, E Christensen, C Jakobs, U Musshoff, J D Fautek, T Deufel, A Ludolph, K Ullrich.   

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Year:  1997        PMID： 9266362     DOI： 10.1023/a:1005342331229

Source DB:  PubMed          Journal:  J Inherit Metab Dis        ISSN： 0141-8955            Impact factor:   4.982


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  10 in total

1.  Hypothesis: a role for quinolinic acid in the neuropathology of glutaric aciduria type I.

Authors:  M P Heyes
Journal:  Can J Neurol Sci       Date:  1987-08       Impact factor: 2.104

2.  Postnatal development of GABA-mediated synaptic inhibition in rat hippocampus.

Authors:  J W Swann; R J Brady; D L Martin
Journal:  Neuroscience       Date:  1989       Impact factor: 3.590

3.  Improved assay of glutaryl-CoA dehydrogenase in cultured cells and liver: application to glutaric aciduria type I.

Authors:  E Christensen
Journal:  Clin Chim Acta       Date:  1983-03-28       Impact factor: 3.786

4.  Organotypic monolayer cultures of nervous tissue.

Authors:  B H Gähwiler
Journal:  J Neurosci Methods       Date:  1981-12       Impact factor: 2.390

5.  Amino acids as central nervous transmitters: the influence of ions, amino acid analogues, and ontogeny on transport systems for L-glutamic and L-aspartic acids and glycine into central nervous synaptosomes of the rat.

Authors:  J P Bennett; W J Logan; S H Snyder
Journal:  J Neurochem       Date:  1973-12       Impact factor: 5.372

6.  Direct observation of the agonist-specific regional vulnerability to glutamate, NMDA, and kainate neurotoxicity in organotypic hippocampal cultures.

Authors:  J J Vornov; R C Tasker; J T Coyle
Journal:  Exp Neurol       Date:  1991-10       Impact factor: 5.330

7.  Inhibition of brain glutamate decarboxylase by glutarate, glutaconate, and beta-hydroxyglutarate: explanation of the symptoms in glutaric aciduria?

Authors:  O Stokke; S I Goodman; P G Moe
Journal:  Clin Chim Acta       Date:  1976-02-02       Impact factor: 3.786

8.  Effects of the epileptogenic agent bicuculline methiodide on membrane currents induced by N-methyl-D-aspartate and kainate (oocyte; Xenopus laevis).

Authors:  U Musshoff; M Madeja; P Bloms-Funke; E J Speckmann
Journal:  Brain Res       Date:  1994-03-07       Impact factor: 3.252

9.  Glutaric aciduria type 1 an atypical presentation together with some observations upon treatment and the possible cause of cerebral damage.

Authors:  J M Land; P Goulder; A Johnson; J Hockaday
Journal:  Neuropediatrics       Date:  1992-12       Impact factor: 1.947

10.  Glutaric aciduria: biochemical and morphologic considerations.

Authors:  S I Goodman; M D Norenberg; R H Shikes; D J Breslich; P G Moe
Journal:  J Pediatr       Date:  1977-05       Impact factor: 4.406
  10 in total
  19 in total

1.  3-Hydroxyglutaric and glutaric acids are neurotoxic through NMDA receptors in vitro.

Authors:  S Kölker; B Ahlemeyer; J Krieglstein; G F Hoffmann
Journal:  J Inherit Metab Dis       Date:  1999-05       Impact factor: 4.982

2.  Glutaric aciduria type I: pathomechanisms of neurodegeneration.

Authors:  K Ullrich; B Flott-Rahmel; P Schluff; U Musshoff; A Das; T Lücke; R Steinfeld; E Christensen; C Jakobs; A Ludolph; A Neu; R Röper
Journal:  J Inherit Metab Dis       Date:  1999-06       Impact factor: 4.982

3.  Inhibition of energy production in vitro by glutaric acid in cerebral cortex of young rats.

Authors:  C G Silva; A R Silva; C Ruschel; C Helegda; A T Wyse; C M Wannmacher; C S Dutra-Filho; M Wajner
Journal:  Metab Brain Dis       Date:  2000-06       Impact factor: 3.584

4.  Infant mice with glutaric acidaemia type I have increased vulnerability to 3-nitropropionic acid toxicity.

Authors:  K B Bjugstad; L S Crnic; S I Goodman; C R Freed
Journal:  J Inherit Metab Dis       Date:  2006-08-30       Impact factor: 4.982

5.  Energy metabolism is compromised in skeletal muscle of rats chronically-treated with glutaric acid.

Authors:  Gustavo da C Ferreira; Patrícia F Schuck; Carolina M Viegas; Anelise Tonin; Alexandra Latini; Carlos S Dutra-Filho; Angela T S Wyse; Clóvis M D Wannmacher; Carmen R Vargas; Moacir Wajner
Journal:  Metab Brain Dis       Date:  2007-01-13       Impact factor: 3.584

6.  Glutaric acid administration impairs energy metabolism in midbrain and skeletal muscle of young rats.

Authors:  Gustavo da C Ferreira; Carolina M Viegas; Patrícia F Schuck; Anelise Tonin; César A J Ribeiro; Daniella de M Coelho; Teresa Dalla-Costa; Alexandra Latini; Angela T S Wyse; Clovis M D Wannmacher; Carmen R Vargas; Moacir Wajner
Journal:  Neurochem Res       Date:  2005-09       Impact factor: 3.996

7.  Biochemistry and bioenergetics of glutaryl-CoA dehydrogenase deficiency.

Authors:  S W Sauer
Journal:  J Inherit Metab Dis       Date:  2007-09-21       Impact factor: 4.982

8.  Neural transplants in patients with Huntington's disease undergo disease-like neuronal degeneration.

Authors:  F Cicchetti; S Saporta; R A Hauser; M Parent; M Saint-Pierre; P R Sanberg; X J Li; J R Parker; Y Chu; E J Mufson; J H Kordower; T B Freeman
Journal:  Proc Natl Acad Sci U S A       Date:  2009-07-20       Impact factor: 11.205

9.  Effects of L-2-hydroxyglutaric acid on various parameters of the glutamatergic system in cerebral cortex of rats.

Authors:  Débora Junqueira; Ana M Brusque; Lisiane O Porciúncula; Liane N Rotta; Céar A J Ribeiro; Marcos E S Frizzo; Carlos S Dutra Filho; Clóvis M D Wannmacher; Angela T S Wyse; Diogo O Souza; Moacir Wajner
Journal:  Metab Brain Dis       Date:  2003-09       Impact factor: 3.584

10.  Age and brain structural related effects of glutaric and 3-hydroxyglutaric acids on glutamate binding to plasma membranes during rat brain development.

Authors:  Karina B Dalcin; Rafael B Rosa; Anna L Schmidt; Juliana S Winter; Guilhian Leipnitz; Carlos S Dutra-Filho; Clóvis M D Wannmacher; Lisiane O Porciúncula; Diogo O Souza; Moacir Wajner
Journal:  Cell Mol Neurobiol       Date:  2007-09-05       Impact factor: 5.046
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