Literature DB >> 9189974

Anaesthetic management of children with Joubert syndrome.

W Habre1, C Sims, M D'Souza.   

Abstract

We report the anaesthetic management of two children with Joubert syndrome. Children with this syndrome have abnormalities of respiratory control due to changes in the brainstem and cerebellum. They are extremely sensitive to the respiratory depressant effects of anaesthetic agents, including nitrous oxide. Anaesthesia using inhalational induction, controlled ventilation, avoidance of opioids, and close postoperative monitoring is recommended.

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Year:  1997        PMID： 9189974     DOI： 10.1046/j.1460-9592.1997.d01-65.x

Source DB:  PubMed          Journal:  Paediatr Anaesth        ISSN： 1155-5645            Impact factor:   2.556


  12 in total

1.  MRI findings in Joubert syndrome.

Authors:  Suhil A Choh; Naseer A Choh; Shabir A Bhat; Majid Jehangir
Journal:  Indian J Pediatr       Date:  2009-01-05       Impact factor: 1.967

2.  Orofacial manifestations and dental considerations in association with Varadi-Papp syndrome: report of a rare case.

Authors:  N Chhabra; A Chhabra; S Tandon
Journal:  Eur Arch Paediatr Dent       Date:  2015-07-10

3.  Nystagmus in a newborn: a manifestation of Joubert syndrome in the neonatal period.

Authors:  Inês Salva; Carolina Albuquerque; Ana Moreira; Catarina Dâmaso
Journal:  BMJ Case Rep       Date:  2016-01-12

4.  Joubert syndrome.

Authors:  Lakshmikanth Halegubbi Karegowda; Poonam Mohan Shenoy; Smiti Sripathi; Mugil Varman
Journal:  BMJ Case Rep       Date:  2014-03-20

5.  Joubert syndrome in a neonate: case report with literature review.

Authors:  Haifa A Bin Dahman; Abdul-Hakeem M Bin Mubaireek; Zain H Alhaddad
Journal:  Sudan J Paediatr       Date:  2016

Review 6.  Healthcare recommendations for Joubert syndrome.

Authors:  Ruxandra Bachmann-Gagescu; Jennifer C Dempsey; Sara Bulgheroni; Maida L Chen; Stefano D'Arrigo; Ian A Glass; Theo Heller; Elise Héon; Friedhelm Hildebrandt; Nirmal Joshi; Dana Knutzen; Hester Y Kroes; Stephen H Mack; Sara Nuovo; Melissa A Parisi; Joseph Snow; Angela C Summers; Jordan M Symons; Wadih M Zein; Eugen Boltshauser; John A Sayer; Meral Gunay-Aygun; Enza Maria Valente; Dan Doherty
Journal:  Am J Med Genet A       Date:  2019-11-11       Impact factor: 2.802

7.  Normal breathing requires preBötzinger complex neurokinin-1 receptor-expressing neurons.

Authors:  P A Gray; W A Janczewski; N Mellen; D R McCrimmon; J L Feldman
Journal:  Nat Neurosci       Date:  2001-09       Impact factor: 24.884

8.  Anesthetic considerations of Joubert syndrome in patients with mitochondrial disease - A case report.

Authors:  Jeong Yeon Kim; Koun Jeong; Ki Seob Han; Ji Eun Park; Mun Gyu Kim; Mi Roung Jun
Journal:  Anesth Pain Med (Seoul)       Date:  2021-04-12

9.  A report of Joubert syndrome in an infant, with literature review.

Authors:  Paramdeep Singh; Jatinder S Goraya; Kavita Saggar; Archana Ahluwalia
Journal:  J Pediatr Neurosci       Date:  2011-01

10.  Anaesthetising an infant with acrocallosal syndrome: An unusual case.

Authors:  Bharathi Hosdurg; Anita Pramod Nair; Jayashree Simha; Suma Sriramanan
Journal:  Indian J Anaesth       Date:  2018-05
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