Literature DB >> 911406

Erythropoietic protoporphyria: juvenile protoporphyrin hepatopathy cirrhosis and death.

D J Cripps, L A Gilbert, S S Goldfarb.   

Abstract

Severe hepatic cirrhosis and failure in erythropoietic protoporphyria is rare. An 11-year-old boy is described who developed protoporphyrin hepatopathy (protoporphyrin 5.75 mg/gm liver wet weight), cirrhosis, and liver failure and died.

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Year:  1977        PMID: 911406     DOI: 10.1016/s0022-3476(77)81027-5

Source DB:  PubMed          Journal:  J Pediatr        ISSN: 0022-3476            Impact factor:   4.406


  4 in total

1.  Phototoxicity of protoporphyrin as related to its subcellular localization in mice livers after short-term feeding with griseofulvin.

Authors:  S Sandberg; I Romslo
Journal:  Biochem J       Date:  1981-07-15       Impact factor: 3.857

2.  An autopsy case of erythropoietic protoporphyria with cholestatic jaundice and hepatic failure, and a review of literature.

Authors:  Y Nakanuma; M Wada; N Kono; H Miyamura; G Ohta
Journal:  Virchows Arch A Pathol Anat Histol       Date:  1981

3.  Protoporphyrin-induced cholestasis in the isolated in situ perfused rat liver.

Authors:  D L Avner; R G Lee; M M Berenson
Journal:  J Clin Invest       Date:  1981-02       Impact factor: 14.808

4.  Pathogenesis and therapy of liver disease in protoporphyria.

Authors:  J R Bloomer
Journal:  Yale J Biol Med       Date:  1979 Jan-Feb
  4 in total

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