BACKGROUND: The occurrence of proptosis at birth is unusual and may be associated with a variety of tumours and structural abnormalities. Congenital orbital teratoma is a rare cause of congenital proptosis. METHODS: A case report is presented of a female infant with gross right proptosis. RESULTS: Computed tomography demonstrated a characteristic multicystic structure with no intracranial involvement. Histological examination found tissues derived from all three germ cell layers, consistent with a congenita orbital teratoma. The tumour was successfully removed preserving the globe and vision. CONCLUSIONS: This report is an example of how early surgical intervention may allow preservation of the globe and vision in some patients with congenital orbital teratoma.
BACKGROUND: The occurrence of proptosis at birth is unusual and may be associated with a variety of tumours and structural abnormalities. Congenital orbital teratoma is a rare cause of congenital proptosis. METHODS: A case report is presented of a female infant with gross right proptosis. RESULTS: Computed tomography demonstrated a characteristic multicystic structure with no intracranial involvement. Histological examination found tissues derived from all three germ cell layers, consistent with a congenita orbital teratoma. The tumour was successfully removed preserving the globe and vision. CONCLUSIONS: This report is an example of how early surgical intervention may allow preservation of the globe and vision in some patients with congenital orbital teratoma.
Authors: D Fugelseth; W B Børke; K Lenes; I Matthews; O D Saugstad; E Thaulow Journal: Arch Dis Child Fetal Neonatal Ed Date: 2005-05 Impact factor: 5.747