Literature DB >> 9083516

Bronchiolitis obliterans in ataxia-telangiectasia.

M Ito1, A Nakagawa, N Hirabayashi, J Asai.   

Abstract

Pulmonary disease was studied in four patients with ataxia-telangiectasia. Immunodeficiency was characterized by lymphopaenia, hypo-gammaglobulinaemia and decreased T-cell response to phytohaemagglutinin stimulation in mixed lymphocyte cultures. All four patients died from respiratory failure. Autopsy revealed that all four patients suffered from bronchiolitis obliterans in all lobes. Immunohistochemical examination demonstrated expression of MHC class II antigens on bronchiolar epithelium. Pulmonary infections in ataxia-telangiectasia patients included a case of mycoplasma pneumonia, one of cytomegalovirus pneumonia and one of Pseudomonas aeruginosa infection. The aetiology and immunological background of bronchiolitis obliterans are discussed. Bronchiolitis obliterans is a characteristic finding in ataxia-telangiectasia and may be due to the underlying immune deficit.

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Mesh：

Year:  1997        PMID： 9083516     DOI： 10.1007/bf01008034

Source DB:  PubMed          Journal:  Virchows Arch        ISSN： 0945-6317            Impact factor:   4.064


  24 in total

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Journal:  Respir Med       Date:  1991-11       Impact factor: 3.415

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Journal:  J Clin Invest       Date:  1988-09       Impact factor: 14.808

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Journal:  Am J Roentgenol Radium Ther Nucl Med       Date:  1973-04

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Journal:  Nature       Date:  1985 Jan 17-23       Impact factor: 49.962

5.  Relative increase of T cells expressing the gamma/delta rather than the alpha/beta receptor in ataxia-telangiectasia.

Authors:  M Carbonari; M Cherchi; R Paganelli; G Giannini; E Galli; C Gaetano; C Papetti; M Fiorilli
Journal:  N Engl J Med       Date:  1990-01-11       Impact factor: 91.245

6.  A role for intestinal T lymphocytes in bronchus mucosal immunity.

Authors:  F J Wallace; A W Cripps; R L Clancy; A J Husband; C S Witt
Journal:  Immunology       Date:  1991-09       Impact factor: 7.397

7.  Lung immunogenicity, rejection, and obliterative bronchiolitis.

Authors:  C M Burke; A R Glanville; J Theodore; E D Robin
Journal:  Chest       Date:  1987-09       Impact factor: 9.410

8.  Obliterative bronchiolitis due to Mycoplasma pneumoniae infection in a child.

Authors:  A F Isles; J Masel; J O'Duffy
Journal:  Pediatr Radiol       Date:  1987

9.  A subset of gamma delta lymphocytes is increased during HIV-1 infection.

Authors:  P De Paoli; D Gennari; P Martelli; G Basaglia; M Crovatto; S Battistin; G Santini
Journal:  Clin Exp Immunol       Date:  1991-02       Impact factor: 4.330

10.  A single ataxia telangiectasia gene with a product similar to PI-3 kinase.

Authors:  K Savitsky; A Bar-Shira; S Gilad; G Rotman; Y Ziv; L Vanagaite; D A Tagle; S Smith; T Uziel; S Sfez; M Ashkenazi; I Pecker; M Frydman; R Harnik; S R Patanjali; A Simmons; G A Clines; A Sartiel; R A Gatti; L Chessa; O Sanal; M F Lavin; N G Jaspers; A M Taylor; C F Arlett; T Miki; S M Weissman; M Lovett; F S Collins; Y Shiloh
Journal:  Science       Date:  1995-06-23       Impact factor: 47.728
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  6 in total

1.  Evaluation and management of pulmonary disease in ataxia-telangiectasia.

Authors:  Sharon A McGrath-Morrow; W Adam Gower; Cynthia Rothblum-Oviatt; Alan S Brody; Claire Langston; Leland L Fan; Maureen A Lefton-Greif; Thomas O Crawford; Michelle Troche; John T Sandlund; Paul G Auwaerter; Blaine Easley; Gerald M Loughlin; John L Carroll; Howard M Lederman
Journal:  Pediatr Pulmonol       Date:  2010-09

2.  Pulmonary function in children and young adults with ataxia telangiectasia.

Authors:  Sharon A McGrath-Morrow; Howard M Lederman; Angela D Aherrera; Maureen A Lefton-Greif; Thomas O Crawford; Timothy Ryan; Jennifer Wright; Joseph M Collaco
Journal:  Pediatr Pulmonol       Date:  2013-02-08

Review 3.  Challenges in pulmonary fibrosis. 2: Bronchiolocentric fibrosis.

Authors:  Jean-François Cordier
Journal:  Thorax       Date:  2007-07       Impact factor: 9.139

Review 4.  Hyper-IgE syndrome and autoimmunity in Mexican children.

Authors:  Marco Yamazaki-Nakashimada; Samuel Zaltzman-Girshevich; Silvestre Garcia de la Puente; Beatriz De Leon-Bojorge; Sara Espinosa-Padilla; Marimar Saez-de-Ocariz; Daniel Carrasco-Daza; Victor Hernandez-Bautista; Lorenzo Pérez-Fernandez; Francisco Espinosa-Rosales
Journal:  Pediatr Nephrol       Date:  2006-06-22       Impact factor: 3.651

Review 5.  Mycoplasma pneumoniae-associated bronchiolitis causing severe restrictive lung disease in adults: report of three cases and literature review.

Authors:  E D Chan; T Kalayanamit; D A Lynch; R Tuder; P Arndt; R Winn; M I Schwarz
Journal:  Chest       Date:  1999-04       Impact factor: 9.410

6.  The natural history of ataxia-telangiectasia (A-T): A systematic review.

Authors:  Emily Petley; Alexander Yule; Shaun Alexander; Shalini Ojha; William P Whitehouse
Journal:  PLoS One       Date:  2022-03-15       Impact factor: 3.752
  6 in total

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