Literature DB >> 9022619

Congenital absence of the uterus and vagina is not commonly transmitted as a dominant genetic trait: outcomes of surrogate pregnancies.

J C Petrozza1, M R Gray, A J Davis, R H Reindollar.   

Abstract

OBJECTIVE: To determine the inheritance pattern of congenital absence of the uterus and vagina in affected women undergoing surrogacy IVF with this disorder.
DESIGN: Retrospective study.
SETTING: A hospital-based reproductive endocrinology and infertility center. PATIENT(S): Women diagnosed with congenital absence of the uterus and vagina undergoing IVF with subsequent transfer of embryos to a surrogate uterus. INTERVENTION(S): Questionnaires were sent to all infertility treatment centers performing surrogate procedures. MAIN OUTCOME MEASURE(S): Number, gender, and frequency of congenital anomalies in progeny. RESULT(S): Thirty-two of 53 surveyed programs responded (60%). One hundred sixty-two IVF cycles were performed, and 34 liveborn children were delivered (half female). No congenital anomalies were found, except for one male child with a middle ear defect and hearing loss. CONCLUSION(S): These results strongly suggest that congenital absence of the uterus and vagina, if genetically transmitted, is not inherited commonly in a dominant fashion.

Entities:  

Mesh:

Year:  1997        PMID: 9022619     DOI: 10.1016/S0015-0282(97)81927-9

Source DB:  PubMed          Journal:  Fertil Steril        ISSN: 0015-0282            Impact factor:   7.329


  14 in total

1.  Creating neovagina using amnion.

Authors:  S K Kathpalia
Journal:  Med J Armed Forces India       Date:  2015-12-31

2.  Genetic analysis of Mayer-Rokitansky-Kuster-Hauser syndrome in a large cohort of families.

Authors:  Lacey S Williams; Durkadin Demir Eksi; Yiping Shen; Amy C Lossie; Lynn P Chorich; Megan E Sullivan; John A Phillips; Munire Erman; Hyung-Goo Kim; Ozgul M Alper; Lawrence C Layman
Journal:  Fertil Steril       Date:  2017-06-07       Impact factor: 7.329

Review 3.  The Mayer-Rokitansky-Küster-Hauser syndrome (congenital absence of uterus and vagina)--phenotypic manifestations and genetic approaches.

Authors:  Daniel Guerrier; Thomas Mouchel; Laurent Pasquier; Isabelle Pellerin
Journal:  J Negat Results Biomed       Date:  2006-01-27

Review 4.  Mayer-Rokitansky-Küster-Hauser (MRKH) syndrome.

Authors:  Karine Morcel; Laure Camborieux; Daniel Guerrier
Journal:  Orphanet J Rare Dis       Date:  2007-03-14       Impact factor: 4.123

5.  Genetic Syndromes and Genes Involved in the Development of the Female Reproductive Tract: A Possible Role for Gene Therapy.

Authors:  Mt Connell; Cm Owen; Jh Segars
Journal:  J Genet Syndr Gene Ther       Date:  2013

6.  A balanced chromosomal translocation involving chromosomes 3 and 16 in a patient with Mayer-Rokitansky-Kuster-Hauser syndrome reveals new candidate genes at 3p22.3 and 16p13.3.

Authors:  Lacey S Williams; Hyung-Goo Kim; Vera M Kalscheuer; J Matthew Tuck; Lynn P Chorich; Megan E Sullivan; Allison Falkenstrom; Richard H Reindollar; Lawrence C Layman
Journal:  Mol Cytogenet       Date:  2016-07-30       Impact factor: 2.009

7.  Müllerian Agenesis Masquerading as Secondary Amenorrhea.

Authors:  Gloria Tavera; Rina Lazebnik
Journal:  Case Rep Pediatr       Date:  2018-07-19

Review 8.  Options for acquiring motherhood in absolute uterine factor infertility; adoption, surrogacy and uterine transplantation.

Authors:  Benjamin P Jones; Niccole Ranaei-Zamani; Saaliha Vali; Nicola Williams; Srdjan Saso; Meen-Yau Thum; Maya Al-Memar; Nuala Dixon; Gillian Rose; Giuliano Testa; Liza Johannesson; Joseph Yazbek; Stephen Wilkinson; J Richard Smith
Journal:  Obstet Gynaecol       Date:  2021-03-19

Review 9.  Mayer-Rokitansky-Kuster-Hauser syndrome: a review.

Authors:  Laura Londra; Farah S Chuong; Lisa Kolp
Journal:  Int J Womens Health       Date:  2015-11-02

Review 10.  Mayer-Rokitansky-Küster-Hauser (MRKH) syndrome: a comprehensive update.

Authors:  Morten Krogh Herlin; Michael Bjørn Petersen; Mats Brännström
Journal:  Orphanet J Rare Dis       Date:  2020-08-20       Impact factor: 4.123

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