Two cases of primary retroperitoneal mucinous cystadenocarcinoma.

Two cases of primary retroperitoneal mucinous cystadenocarcinoma of the ovarian type in the presence of bilateral normal ovaries are reported. Benign, borderline, and malignant mucinous epithelium were present in both tumors; no separate ovarian tissue was identified. In addition to removal of the tumor, the uterus and both ovaries were removed and the patients are well with no evidence of disease at 30 and 15 months. Only 10 cases of primary retroperitoneal mucinous cystadenocarcinoma have been reported in the English literature and these are reviewed. The outcome of these limited number of cases suggests that removal of both ovaries and the uterus in addition to extirpation of the retroperitoneal tumor, even though the uterus and ovaries are normal, may improve the prognosis.