Literature DB >> 87500

Neutral lipid and sphingolipid composition of the brain of a patient with membranous lipodystrophy.

Y Ohtani, S Miura, Y Tamai, H Kojima, H Kashima.   

Abstract

Lipids were extracted from brains of a patient with membranous lipodystrophy (ML) and three normal patients and the neutral lipid and sphingolipid constituents were investigated. The storage of a large amount of free fatty acid was observed in the ML brain, but no cholesterol ester was found. Total lipid, cholesterol and cerebroside contents were slightly decreased in the white matter of the ML brain. The composition of free and sphingolipid fatty acids did not differ between ML and normal brains.

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Year:  1979        PMID： 87500     DOI： 10.1007/BF00313947

Source DB:  PubMed          Journal:  J Neurol        ISSN： 0340-5354            Impact factor:   4.849


  11 in total

1.  Phosphorus assay in column chromatography.

Authors:  G R BARTLETT
Journal:  J Biol Chem       Date:  1959-03       Impact factor: 5.157

2.  A case of Jakob-Creutzfeldt diseases. 2. Analysis of some constituents of the brain of a patient with Jakob-Creutzfeldt disease.

Authors:  S R KOREY; R KATZMAN; J ORLOFF
Journal:  J Neuropathol Exp Neurol       Date:  1961-01       Impact factor: 3.685

3.  Simple rapid microtechnic for serum total cholesterol.

Authors:  B ZAK
Journal:  Am J Clin Pathol       Date:  1957-05       Impact factor: 2.493

4.  A simple method for the isolation and purification of total lipides from animal tissues.

Authors:  J FOLCH; M LEES; G H SLOANE STANLEY
Journal:  J Biol Chem       Date:  1957-05       Impact factor: 5.157

5.  Alterations in the composition of brain lipids in patients with Creutzfeldt-Jakob disease.

Authors:  Y Tamai; H Kojima; F Ikuta; T Kumanishi
Journal:  J Neurol Sci       Date:  1978-01       Impact factor: 3.181

6.  Neuropsychiatric and genetic aspects of a new hereditary disease characterized by progressive dementia and lipomembranous polycystic osteodysplasia.

Authors:  H P Hakola
Journal:  Acta Psychiatr Scand Suppl       Date:  1972

7.  A lipid metabolic disease-"membranous lipodystrophy"-an autopsy case demonstrating numerous peculiar membrane-structures composed of compound lipid in bone and bone marrow and various adipose tissues.

Authors:  T Nasu; Y Tsukahara; K Terayama
Journal:  Acta Pathol Jpn       Date:  1973-08

8.  The pattern of mammalian brain gangliosides. II. Evaluation of the extraction procedures, postmortem changes and the effect of formalin preservation.

Authors:  K Suzuki
Journal:  J Neurochem       Date:  1965-07       Impact factor: 5.372

9.  Improved reagent for trimethylsilylation of sphingolipid bases.

Authors:  H E Carter; R C Gaver
Journal:  J Lipid Res       Date:  1967-07       Impact factor: 5.922

10.  Fatty acid composition of cholesterol esters in brains of patients with Schilder's disease, G M1 -gangliosidosis and Tay-Sachs disease, and its possible relationship to the -position fatty acids of lecithin.

Authors:  Y Eto; K Suzuki
Journal:  J Neurochem       Date:  1971-06       Impact factor: 5.372
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  4 in total

1.  Ultrastructural demonstration of Maclura pomifera agglutinin binding sites in the membranocystic lesions of membranous lipodystrophy (Nasu-Hakola disease).

Authors:  I Kitajima; T Suganuma; F Murata; K Nagamatsu
Journal:  Virchows Arch A Pathol Anat Histopathol       Date:  1988

2.  Radiologic bone changes of polycystic lipomembranous osteodysplasia with sclerosing leukoencephalopathy.

Authors:  P Mäkelä; O Järví; P Hakola; P Virtama
Journal:  Skeletal Radiol       Date:  1982       Impact factor: 2.199

3.  Ultrastructural lipid and glycoconjugate cytochemistry of membranous lipodystrophy (Nasu-Hakola disease).

Authors:  Y Mii; Y Miyauchi; T Yoshikawa; K Honoki; M Aoki; M Tsutsumi; H Maruyama; M Funauchi; Y Konishi; S Tamai
Journal:  Virchows Arch A Pathol Anat Histopathol       Date:  1991

Review 4.  Nasu-Hakola disease (polycystic lipomembranous osteodysplasia with sclerosing leukoencephalopathy--PLOSL): a dementia associated with bone cystic lesions. From clinical to genetic and molecular aspects.

Authors:  Marino Muxfeldt Bianchin; Heraldo M Capella; Daniel Loureiro Chaves; Mário Steindel; Edmundo C Grisard; Gerson Gandi Ganev; João Péricles da Silva Júnior; Schaeffer Neto Evaldo; Mônica Aparecida Poffo; Roger Walz; Carlos G Carlotti Júnior; Américo C Sakamoto
Journal:  Cell Mol Neurobiol       Date:  2004-02       Impact factor: 5.046
  4 in total

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