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20 in total

1. The endoplasmic reticulum as a protein-folding compartment.

Authors: A Helenius; T Marquardt; I Braakman
Journal: Trends Cell Biol Date: 1992-08 Impact factor: 20.808

2. Multiple serum protein abnormalities in carbohydrate-deficient glycoprotein syndrome: pathognomonic finding of two-dimensional electrophoresis?

Authors: H H Harrison; K L Miller; M D Harbison; A E Slonim
Journal: Clin Chem Date: 1992-07 Impact factor: 8.327

3. Normal N-oligosaccharyltransferase activity in fibroblasts from patients with carbohydrate-deficient glycoprotein syndrome.

Authors: R Knauer; L Lehle; F Hanefeld; K von Figura
Journal: J Inherit Metab Dis Date: 1994 Impact factor: 4.982

4. The primary glycosylation defect in class E Thy-1-negative mutant mouse lymphoma cells is an inability to synthesize dolichol-P-mannose.

Authors: A Chapman; K Fujimoto; S Kornfeld
Journal: J Biol Chem Date: 1980-05-25 Impact factor: 5.157

5. Carbohydrate-deficient glycoprotein syndrome: not an N-linked oligosaccharide processing defect, but an abnormality in lipid-linked oligosaccharide biosynthesis?

Authors: L D Powell; K Paneerselvam; R Vij; S Diaz; A Manzi; N Buist; H Freeze; A Varki
Journal: J Clin Invest Date: 1994-11 Impact factor: 14.808

6. Sugar chains of serum transferrin from patients with carbohydrate deficient glycoprotein syndrome. Evidence of asparagine-N-linked oligosaccharide transfer deficiency.

Authors: K Yamashita; H Ideo; T Ohkura; K Fukushima; I Yuasa; K Ohno; K Takeshita
Journal: J Biol Chem Date: 1993-03-15 Impact factor: 5.157

7. Electrospray ionization-mass spectrometric analysis of serum transferrin isoforms in patients with carbohydrate-deficient glycoprotein syndrome.

Authors: K Yamashita; T Ohkura; H Ideo; K Ohno; M Kanai
Journal: J Biochem Date: 1993-12 Impact factor: 3.387

8. Intracellular transport of soluble and membrane-bound glycoproteins: folding, assembly and secretion of anchor-free influenza hemagglutinin.

Authors: I Singh; R W Doms; K R Wagner; A Helenius
Journal: EMBO J Date: 1990-03 Impact factor: 11.598

9. Misfolding and aggregation of newly synthesized proteins in the endoplasmic reticulum.

Authors: T Marquardt; A Helenius
Journal: J Cell Biol Date: 1992-05 Impact factor: 10.539

10. Membrane glycoprotein folding, oligomerization and intracellular transport: effects of dithiothreitol in living cells.

Authors: U Tatu; I Braakman; A Helenius
Journal: EMBO J Date: 1993-05 Impact factor: 11.598

2 in total

1. Analysis of glycosylation in CDG-Ia fibroblasts by fluorophore-assisted carbohydrate electrophoresis: implications for extracellular glucose and intracellular mannose 6-phosphate.

Authors: Ningguo Gao; Jie Shang; Mark A Lehrman
Journal: J Biol Chem Date: 2005-02-11 Impact factor: 5.157

2. A zebrafish model of PMM2-CDG reveals altered neurogenesis and a substrate-accumulation mechanism for N-linked glycosylation deficiency.

Authors: Abigail Cline; Ningguo Gao; Heather Flanagan-Steet; Vandana Sharma; Sabrina Rosa; Roberto Sonon; Parastoo Azadi; Kirsten C Sadler; Hudson H Freeze; Mark A Lehrman; Richard Steet
Journal: Mol Biol Cell Date: 2012-09-05 Impact factor: 4.138

2 in total