Literature DB >> 8739961

Impaired peroxisomal fatty acid oxidation in human skin fibroblasts with a mitochondrial acylcarnitine/carnitine translocase deficiency.

B S Jakobs1, R J Wanders.   

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Year:  1996        PMID: 8739961     DOI: 10.1007/bf01799425

Source DB:  PubMed          Journal:  J Inherit Metab Dis        ISSN: 0141-8955            Impact factor:   4.982


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  4 in total

Review 1.  Peroxisomal lipid metabolism.

Authors:  J K Reddy; G P Mannaerts
Journal:  Annu Rev Nutr       Date:  1994       Impact factor: 11.848

2.  Carnitine-acylcarnitine translocase deficiency with severe hypoglycemia and auriculo ventricular block. Translocase assay in permeabilized fibroblasts.

Authors:  S V Pande; M Brivet; A Slama; F Demaugre; C Aufrant; J M Saudubray
Journal:  J Clin Invest       Date:  1993-03       Impact factor: 14.808

3.  Fatty acid beta-oxidation in peroxisomes and mitochondria: the first, unequivocal evidence for the involvement of carnitine in shuttling propionyl-CoA from peroxisomes to mitochondria.

Authors:  B S Jakobs; R J Wanders
Journal:  Biochem Biophys Res Commun       Date:  1995-08-24       Impact factor: 3.575

Review 4.  Disorders of mitochondrial long-chain fatty acid oxidation.

Authors:  R J Pollitt
Journal:  J Inherit Metab Dis       Date:  1995       Impact factor: 4.982

  4 in total
  1 in total

1.  Studies of Secondary Melanoma on C57BL/6J Mouse Liver Using 1H NMR Metabolomics.

Authors:  Ju Feng; Nancy G Isern; Sarah D Burton; Jian Zhi Hu
Journal:  Metabolites       Date:  2013-10-31
  1 in total

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