Literature DB >> 8739955

Inhibitory effect of 3-hydroxyacyl-CoAs and other long-chain fatty acid beta-oxidation intermediates on mitochondrial oxidative phosphorylation.

F V Ventura1, J P Ruiter, L Ijlst, I T de Almeida, R J Wanders.   

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Year:  1996        PMID: 8739955     DOI: 10.1007/bf01799419

Source DB:  PubMed          Journal:  J Inherit Metab Dis        ISSN: 0141-8955            Impact factor:   4.982


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  6 in total

1.  Reversible inhibition of mitochondrial adenosine diphosphate phosphorylation by long chain acyl coenzyme A esters.

Authors:  S V Pande; M C Blanchaer
Journal:  J Biol Chem       Date:  1971-01-25       Impact factor: 5.157

2.  3-Hydroxydicarboxylic aciduria due to long-chain 3-hydroxyacyl-coenzyme A dehydrogenase deficiency associated with sudden neonatal death: protective effect of medium-chain triglyceride treatment.

Authors:  M Duran; R J Wanders; J P de Jager; L Dorland; L Bruinvis; D Ketting; L Ijlst; F J van Sprang
Journal:  Eur J Pediatr       Date:  1991-01       Impact factor: 3.183

3.  Acute fatty liver of pregnancy and long-chain 3-hydroxyacyl-coenzyme A dehydrogenase deficiency.

Authors:  W R Treem; P Rinaldo; D E Hale; C A Stanley; D S Millington; J S Hyams; S Jackson; D M Turnbull
Journal:  Hepatology       Date:  1994-02       Impact factor: 17.425

4.  Peroxisomal fatty acid beta-oxidation in relation to the accumulation of very long chain fatty acids in cultured skin fibroblasts from patients with Zellweger syndrome and other peroxisomal disorders.

Authors:  R J Wanders; C W van Roermund; M J van Wijland; R B Schutgens; J Heikoop; H van den Bosch; A W Schram; J M Tager
Journal:  J Clin Invest       Date:  1987-12       Impact factor: 14.808

5.  Studies on mitochondrial oxidative phosphorylation in permeabilized human skin fibroblasts: application to mitochondrial encephalomyopathies.

Authors:  R J Wanders; J P Ruiter; F A Wijburg
Journal:  Biochim Biophys Acta       Date:  1993-06-19

6.  Inhibition of oxidative phosphorylation by palmitoyl-CoA in digitonin permeabilized fibroblasts: implications for long-chain fatty acid beta-oxidation disorders.

Authors:  F V Ventura; J P Ruiter; L Ijlst; I T Almeida; R J Wanders
Journal:  Biochim Biophys Acta       Date:  1995-08-15
  6 in total
  11 in total

1.  Time course of acylcarnitine elevation in neonatal intrahepatic cholestasis caused by citrin deficiency.

Authors:  Ni-Chung Lee; Yin-Hsiu Chien; Keiko Kobayashi; Takeyori Saheki; Huey-Ling Chen; Pao-Chin Chiu; Yen-Hsuan Ni; Mei-Hwei Chang; Wuh-Liang Hwu
Journal:  J Inherit Metab Dis       Date:  2006-05-30       Impact factor: 4.982

2.  A secondary respiratory chain defect in a patient with Fanconi-Bickel syndrome.

Authors:  M H Odièvre; A Lombès; P Dessemme; R Santer; M Brivet; B Chevallier; B Lagardère; M Odièvre
Journal:  J Inherit Metab Dis       Date:  2002-09       Impact factor: 4.982

Review 3.  Inhibitors of succinate: quinone reductase/Complex II regulate production of mitochondrial reactive oxygen species and protect normal cells from ischemic damage but induce specific cancer cell death.

Authors:  Stephen J Ralph; Rafael Moreno-Sánchez; Jiri Neuzil; Sara Rodríguez-Enríquez
Journal:  Pharm Res       Date:  2011-08-24       Impact factor: 4.200

Review 4.  Acute fatty liver of pregnancy: an update on mechanisms.

Authors:  Sathish Kumar Natarajan; Kavitha R Thangaraj; Ashish Goel; C E Eapen; K A Balasubramanian; Anup Ramachandran
Journal:  Obstet Med       Date:  2011-07-04

5.  Long-chain 3-hydroxy fatty acids accumulating in long-chain 3-hydroxyacyl-CoA dehydrogenase and mitochondrial trifunctional protein deficiencies uncouple oxidative phosphorylation in heart mitochondria.

Authors:  Anelise M Tonin; Alexandre U Amaral; Estela N B Busanello; Mateus Grings; Roger F Castilho; Moacir Wajner
Journal:  J Bioenerg Biomembr       Date:  2012-10-13       Impact factor: 2.945

6.  Evidence that antioxidants prevent the inhibition of Na+,K(+)-ATPase activity induced by octanoic acid in rat cerebral cortex in vitro.

Authors:  Dênis R de Assis; César A J Ribeiro; Rafael B Rosa; Patricia F Schuck; Karina B Dalcin; Carmen R Vargas; Clóvis M D Wannmacher; Carlos S Dutra-Filho; Angela T S Wyse; Paz Briones; Moacir Wajner
Journal:  Neurochem Res       Date:  2003-08       Impact factor: 3.996

7.  Acute respiratory distress syndrome in long-chain 3-hydroxyacyl-CoA dehydrogenase and mitochondrial trifunctional protein deficiencies.

Authors:  C T Lundy; J P H Shield; E A Kvittingen; O J Vinorum; E R Trimble; A A M Morris
Journal:  J Inherit Metab Dis       Date:  2003       Impact factor: 4.982

8.  Lactic acidosis in long-chain fatty acid beta-oxidation disorders.

Authors:  F V Ventura; J P Ruiter; L IJlst; I T de Almeida; R J Wanders
Journal:  J Inherit Metab Dis       Date:  1998-08       Impact factor: 4.982

9.  High activity of fatty acid oxidation enzymes in human placenta: implications for fetal-maternal disease.

Authors:  N A Oey; M E J den Boer; J P N Ruiter; R J A Wanders; M Duran; H R Waterham; K Boer; J A M van der Post; F A Wijburg
Journal:  J Inherit Metab Dis       Date:  2003       Impact factor: 4.750

Review 10.  Mitochondrial dysfunction in fatty acid oxidation disorders: insights from human and animal studies.

Authors:  Moacir Wajner; Alexandre Umpierrez Amaral
Journal:  Biosci Rep       Date:  2015-11-20       Impact factor: 3.840

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