Literature DB >> 8726652

Incontinentia pigmenti and Behçet's disease: a case of impaired neutrophil chemotaxis.

M Endoh1, H Yokozeki, R Maruyama, T Matsunaga, I Katayama, K Nishioka.   

Abstract

We describe a patient with incontinentia pigmenti who developed the clinical picture of intestinal Behçet's disease. Diagnosis of Behçet's disease was base on a recurrent genital and oral ulcer and a positive HLA-B51. Impaired neutrophil chemotactic activity and an elevated plasma IL-6 level were found. Chromosomal study revealed no abnormality in the patient or her family. We discuss the possibility that there are common immunological abnormalities in the two syndromes.

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Year:  1996        PMID: 8726652     DOI: 10.1159/000246388

Source DB:  PubMed          Journal:  Dermatology        ISSN: 1018-8665            Impact factor:   5.366


  2 in total

1.  Incontinentia pigmenti and bipolar aphthosis: an unusual combination.

Authors:  G Márquez Balbás; M A González-Enseñat; A Vicente; L Creus-Vila; J Antón; P Umbert-Millet
Journal:  ISRN Dermatol       Date:  2011-03-07

Review 2.  Paediatric Behçet's Disease: A Comprehensive Review with an Emphasis on Monogenic Mimics.

Authors:  Ovgu Kul Cinar; Micol Romano; Ferhat Guzel; Paul A Brogan; Erkan Demirkaya
Journal:  J Clin Med       Date:  2022-02-26       Impact factor: 4.241

  2 in total

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