Extranodal sinus histiocytosis with massive lymphadenopathy: isolated central nervous system involvement mimicking meningioma.

We present the fifth reported case of extranodal sinus histiocytosis with massive lymphadenopathy (SHML) isolated in the central nervous system. This case emphasizes the importance of recognizing the clinical and radiographic presentation of SHML and shows that immunohistochemical evaluation is required for definitive diagnosis.