Literature DB >> 8636833

Successful medical treatment of severely decompensated Wilson disease.

E E Santos Silva1, J Sarles, J P Buts, E M Sokal.   

Abstract

Delayed response to medical treatment sometimes leads to unnecessary liver transplantation in patients with severely decompensated Wilson disease. We report the course of five patients (mean age 13.4 years, range 11 to 15 years) with severely decompensated Wilson disease who were successfully treated medically. Prothrombin time improved after a minimum of 1 month and returned to normal within 3 months to 1 year or more.

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Year:  1996        PMID: 8636833     DOI: 10.1016/s0022-3476(96)70412-2

Source DB:  PubMed          Journal:  J Pediatr        ISSN: 0022-3476            Impact factor:   4.406


  10 in total

Review 1.  Recent advances: hepatology.

Authors:  M McCarthy; M L Wilkinson
Journal:  BMJ       Date:  1999-05-08

Review 2.  A review and current perspective on Wilson disease.

Authors:  Mallikarjun Patil; Keyur A Sheth; Adarsh C Krishnamurthy; Harshad Devarbhavi
Journal:  J Clin Exp Hepatol       Date:  2013-07-06

Review 3.  Evolving perspectives in Wilson disease: diagnosis, treatment and monitoring.

Authors:  Karl Heinz Weiss; Wolfgang Stremmel
Journal:  Curr Gastroenterol Rep       Date:  2012-02

4.  Liver transplantation for inborn errors of liver metabolism.

Authors:  Efienne M Sokal
Journal:  J Inherit Metab Dis       Date:  2006 Apr-Jun       Impact factor: 4.982

Review 5.  Treatment of Wilson's disease: what are the relative roles of penicillamine, trientine, and zinc supplementation?

Authors:  M L Schilsky
Journal:  Curr Gastroenterol Rep       Date:  2001-02

Review 6.  Combination Therapy Using Chelating Agent and Zinc for Wilson's Disease.

Authors:  Jui-Chi Chen; Cheng-Hung Chuang; Jing-Doo Wang; Chi-Wei Wang
Journal:  J Med Biol Eng       Date:  2015-11-19       Impact factor: 1.553

Review 7.  Advances in Treatment of Wilson Disease.

Authors:  Annu Aggarwal; Mohit Bhatt
Journal:  Tremor Other Hyperkinet Mov (N Y)       Date:  2018-02-28

Review 8.  Chelation therapy in liver diseases of childhood: Current status and response.

Authors:  Jayendra Seetharaman; Moinak Sen Sarma
Journal:  World J Hepatol       Date:  2021-11-27

9.  Wilson disease developing osteoarthritic pain in severe acute liver failure: A case report.

Authors:  Jun Kido; Shirou Matsumoto; Keishin Sugawara; Kimitoshi Nakamura
Journal:  World J Hepatol       Date:  2019-07-27

Review 10.  Wilson disease in children and young adults - State of the art.

Authors:  Atchariya Chanpong; Anil Dhawan
Journal:  Saudi J Gastroenterol       Date:  2022 Jan-Feb       Impact factor: 2.485

  10 in total

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