Literature DB >> 8566880

Diagnostic approach to and follow-up of difficult cases of AL amyloidosis.

V Perfetti1, P Garini, M C Vignarelli, M G Marinone, I Zorzoli, G Merlini.   

Abstract

BACKGROUND: Routine electrophoretic analysis fails to detect a monoclonal component (MC) in a considerable portion of AL amyloidosis patients. We investigated whether the combination of immunofixation (IF) on agarose gel electrophoresis and bone marrow plasma cell (BMPC) light chain kappa/lambda ratio analysis could contribute to diagnosis in these cases. The possible use of the BMPC kappa/lambda ratio in monitoring the clone was also investigated.
METHODS: We performed BMPC kappa/lambda ratio analysis and IF of serum and urine in 16 selected patients with no detectable MC at routine analysis, despite clinical features suggestive of primary amyloidosis. An anti-idiotypic monoclonal antibody specific for the amyloidogenic immunoglobulin and the BMPC kappa/lambda ratio were used to monitor the clone in a patient who underwent autologous peripheral blood stem cell transplantation.
RESULTS: Abnormal kappa/lambda ratios were found in 14 (sensitivity 87.5%), and a MC in 12 (sensitivity 75%). Combination of the two analyses confirmed diagnosis in all cases. In one patient changes in the size of the clone, monitored on serial bone marrow aspirates by an anti-idiotypic antibody, paralleled variations of the kappa/lambda ratio.
CONCLUSIONS: This study demonstrates that the combined use of IF and the BMPC kappa/lambda ratio is extremely powerful in AL amyloidosis. In addition, the BMPC kappa/lambda ratio should be considered for monitoring the amyloidogenic clone when serum or urine MC is not quantifiable.

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Year:  1995        PMID: 8566880

Source DB:  PubMed          Journal:  Haematologica        ISSN: 0390-6078            Impact factor:   9.941


  4 in total

1.  Widespread cardiovascular autonomic dysfunction in primary amyloidosis: does spontaneous hyperventilation have a compensatory role against postural hypotension?

Authors:  L Bernardi; C Passino; C Porta; E Anesi; G Palladini; G Merlini
Journal:  Heart       Date:  2002-12       Impact factor: 5.994

2.  Translocation T(4;14)(p16.3;q32) is a recurrent genetic lesion in primary amyloidosis.

Authors:  V Perfetti; A M Coluccia; D Intini; U Malgeri; M C Vignarelli; S Casarini; G Merlini; A Neri
Journal:  Am J Pathol       Date:  2001-05       Impact factor: 4.307

Review 3.  Deposition-associated diseases related with a monoclonal compound.

Authors:  M J Molina-Garrido; C Guillén-Ponce; A Mora; M Guirado-Risueño; M A Molina; M J Molina; A Carrato
Journal:  Clin Transl Oncol       Date:  2007-12       Impact factor: 3.405

4.  Skin involvement in primary systemic amyloidosis.

Authors:  Susheel Kumar; Rimi Som Sengupta; Nandita Kakkar; Aman Sharma; Surjit Singh; Subhash Varma
Journal:  Mediterr J Hematol Infect Dis       Date:  2013-01-02       Impact factor: 2.576

  4 in total

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