Literature DB >> 8529680

A fatal case of portal hypertension complicating systemic mastocytosis in an adolescent.

H S Fonga-Djimi1, F Gottrand, M Bonnevalle, J P Farriaux.   

Abstract

Portal hypertension was observed in a 17-year-old girl with urticaria pigmentosa since 2 months of age. Liver biopsies showed portal and sinusoidal infiltration with mast cells although spleen biopsies showed only fibrosis. CONCLUSION. Portal hypertension is a complication of systemic mastocytosis that can lead to death. Treatment with interferon alpha might be effective.

Entities:  

Mesh：

Year:  1995        PMID： 8529680     DOI： 10.1007/bf01959789

Source DB:  PubMed          Journal:  Eur J Pediatr        ISSN： 0340-6199            Impact factor:   3.183


  14 in total

Review 1.  [Systemic mastocytosis disclosed by rupture of esophageal varices].

Authors:  C Silvain; P Levillain; P Mouton; M Carretier; P Babin; M Beauchant
Journal:  Gastroenterol Clin Biol       Date:  1989-10

Review 2.  Pediatric mastocytosis.

Authors:  B V Kettelhut; D D Metcalfe
Journal:  J Invest Dermatol       Date:  1991-03       Impact factor: 8.551

3.  Portal hypertension and ascites in systemic mastocytosis.

Authors:  M N Narayanan; J A Liu Yin; S Azzawi; T W Warnes; W P Turck
Journal:  Postgrad Med J       Date:  1989-06       Impact factor: 2.401

Review 4.  Systemic mast cell disease. Analysis of 58 cases and literature review.

Authors:  W D Travis; C Y Li; E J Bergstralh; L T Yam; R G Swee
Journal:  Medicine (Baltimore)       Date:  1988-11       Impact factor: 1.889

5.  Intractable ascites in systemic mastocytosis treated by portal diversion.

Authors:  P Bonnet; C Smadja; A M Szekely; Y Delage; Y Calmus; R Poupon; D Franco
Journal:  Dig Dis Sci       Date:  1987-02       Impact factor: 3.199

6.  Hepatic involvement in systemic mast cell disease.

Authors:  L T Yam; C H Chan; C Y Li
Journal:  Am J Med       Date:  1986-05       Impact factor: 4.965

7.  Variceal bleeding, hypersplenism, and systemic mastocytosis. Pathophysiology and management.

Authors:  B E Sumpio; G O'Leary; R J Gusberg
Journal:  Arch Surg       Date:  1988-06

8.  Portal hypertension associated with systemic mastocytosis and splenomegaly.

Authors:  S Grundfest; A M Cooperman; R Ferguson; S Benjamin
Journal:  Gastroenterology       Date:  1980-02       Impact factor: 22.682

9.  Systemic mastocytosis with portal hypertension. Autopsy findings and ultrastructural study of the liver.

Authors:  L Ghandur-Mnaymneh; E Gould
Journal:  Arch Pathol Lab Med       Date:  1985-01       Impact factor: 5.534

10.  Portal hypertension in systemic mastocytosis.

Authors:  J P Capron; D Lebrec; C Degott; D Chivrac; B Coevoet; J Delobel
Journal:  Gastroenterology       Date:  1978-03       Impact factor: 22.682
View more
  2 in total

Review 1.  Gastrointestinal manifestations of systemic mastocytosis.

Authors:  Jason K Lee; Scott J Whittaker; Robert A Enns; Peter Zetler
Journal:  World J Gastroenterol       Date:  2008-12-07       Impact factor: 5.742

2.  Hepatoportal venopathy due to disseminated Mycobacterium avium complex infection in a child with IFN-gamma receptor 2 deficiency.

Authors:  Amy V Rapkiewicz; Smita Y Patel; Steven M Holland; David E Kleiner
Journal:  Virchows Arch       Date:  2007-06-07       Impact factor: 4.064
  2 in total

北京卡尤迪生物科技股份有限公司 © 2022-2023.