Literature DB >> 8488882

Inguinal hernia and atrial septal defect in Tel Hashomer camptodactyly syndrome: report of a new case expanding the phenotypic spectrum of the disease.

P Franceschini1, M P Vardeu, F Signorile, A Testa, A Guala, D Franceschini, L Dalforno.   

Abstract

We report on a girl with Tel Hashomer camptodactyly syndrome (THCS) born to first-cousin parents. In addition to the usual findings, the patient had bilateral inguinal hernia and atrial septal defect, not previously described as component manifestations of the syndrome. The present description expands the phenotypic spectrum of the syndrome and gives new support to the hypothesized pleiotropic effects of the THCS gene on connective tissue.

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Year:  1993        PMID: 8488882     DOI: 10.1002/ajmg.1320460320

Source DB:  PubMed          Journal:  Am J Med Genet        ISSN: 0148-7299


  2 in total

1.  Prenatal diagnosis of limb abnormalities: role of fetal ultrasonography.

Authors:  Santina Ermito; Angela Dinatale; Sabina Carrara; Alessandro Cavaliere; Laura Imbruglia; Stefania Recupero
Journal:  J Prenat Med       Date:  2009-04

Review 2.  The status of dermatoglyphics as a biomarker of Tel Hashomer camptodactyly syndrome: a review of the literature.

Authors:  Buddhika T B Wijerathne; Robert J Meier; Suneth B Agampodi
Journal:  J Med Case Rep       Date:  2016-09-20
  2 in total

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