Literature DB >> 8411985

Molecular basis of lysosomal accumulation of subunit c of mitochondrial ATP synthase in neuronal ceroid-lipofuscinosis.

J Ezaki1, L S Wolfe, E Kominami.   

Abstract

Entities:  

Mesh：

Substances：

Year:  1993        PMID： 8411985     DOI： 10.1007/bf00710269

Source DB:  PubMed          Journal:  J Inherit Metab Dis        ISSN： 0141-8955            Impact factor:   4.982


× No keyword cloud information.
  7 in total

1.  The sequence of the major protein stored in ovine ceroid lipofuscinosis is identical with that of the dicyclohexylcarbodiimide-reactive proteolipid of mitochondrial ATP synthase.

Authors:  I M Fearnley; J E Walker; R D Martinus; R D Jolly; K B Kirkland; G J Shaw; D N Palmer
Journal:  Biochem J       Date:  1990-06-15       Impact factor: 3.857

2.  Infantile form of neuronal ceroid lipofuscinosis (CLN1) maps to the short arm of chromosome 1.

Authors:  I Järvelä; J Schleutker; L Haataja; P Santavuori; L Puhakka; T Manninen; A Palotie; L A Sandkuijl; M Renlund; R White
Journal:  Genomics       Date:  1991-01       Impact factor: 5.736

Review 3.  Lysosomal storage of the DCCD reactive proteolipid subunit of mitochondrial ATP synthase in human and ovine ceroid lipofuscinoses.

Authors:  D N Palmer; I M Fearnley; S M Medd; J E Walker; R D Martinus; S L Bayliss; N A Hall; B D Lake; L S Wolfe; R D Jolly
Journal:  Adv Exp Med Biol       Date:  1989       Impact factor: 2.622

4.  Specific storage of subunit c of mitochondrial ATP synthase in lysosomes of neuronal ceroid lipofuscinosis (Batten's disease).

Authors:  E Kominami; J Ezaki; D Muno; K Ishido; T Ueno; L S Wolfe
Journal:  J Biochem       Date:  1992-02       Impact factor: 3.387

5.  Sequestration of cytoplasmic enzymes in an autophagic vacuole-lysosomal system induced by injection of leupeptin.

Authors:  E Kominami; S Hashida; E A Khairallah; N Katunuma
Journal:  J Biol Chem       Date:  1983-05-25       Impact factor: 5.157

6.  Lysosomal storage of subunit c of mitochondrial ATP synthase in Batten's disease (ceroid-lipofuscinosis).

Authors:  N A Hall; B D Lake; N N Dewji; A D Patrick
Journal:  Biochem J       Date:  1991-04-01       Impact factor: 3.857

7.  Ovine ceroid lipofuscinosis. The major lipopigment protein and the lipid-binding subunit of mitochondrial ATP synthase have the same NH2-terminal sequence.

Authors:  D N Palmer; R D Martinus; S M Cooper; G G Midwinter; J C Reid; R D Jolly
Journal:  J Biol Chem       Date:  1989-04-05       Impact factor: 5.157
  7 in total
  2 in total

1.  Batten disease (ceroid-lipofuscinosis): the enigma of subunit c of mitochondrial ATP synthase accumulation.

Authors:  R D Jolly
Journal:  Neurochem Res       Date:  1995-11       Impact factor: 3.996

2.  Elevated levels of neutrophil 4-hydroxynonenal in canine neuronal ceroid-lipofuscinosis and human immortalized lymphocytes of NCL patients.

Authors:  A N Siakotos; F J van Kuijk; J A Tischfield
Journal:  J Inherit Metab Dis       Date:  1993       Impact factor: 4.982
  2 in total

北京卡尤迪生物科技股份有限公司 © 2022-2023.