Literature DB >> 8383474

Extrarenal Wilms' tumor. Unusual presentation in the lumbosacral region.

J B Fahner1, R Switzer, D R Freyer, J D Mann, R J Mann.   

Abstract

True extrarenal Wilms' tumor is a rare malignant neoplasm most frequently presenting in the retroperitoneal or inguinal regions. We report an unusual subcutaneous lumbosacral (LS) region extrarenal Wilms' tumor without associated teratomatous tumor elements or associated neural tube defect in a 2 1/2-year-old girl. Pathologic review revealed features of true extrarenal Wilms' tumor, and the patient remains in complete remission following surgery and combination chemotherapy. This report illustrates the importance of early surgical intervention and pathologic examination of similar soft tissue masses in children.

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Year:  1993        PMID: 8383474

Source DB:  PubMed          Journal:  Am J Pediatr Hematol Oncol        ISSN: 0192-8562


  3 in total

1.  Primary lumbosacral Wilms tumor associated with diastematomyelia and occult spinal dysraphism. A report of a rare case and a short review of literature.

Authors:  M C Sharma; P Sarat Chandra; S Goel; V Gupta; C Sarkar
Journal:  Childs Nerv Syst       Date:  2004-11-20       Impact factor: 1.475

Review 2.  Extra-renal Wilms' tumour--is it different?

Authors:  Jayant Sastri; Rupal Dedhia; Siddharth Laskar; Tanuja Shet; Purna Kurkure; Maryann Muckaden
Journal:  Pediatr Nephrol       Date:  2006-03-07       Impact factor: 3.714

3.  18Fluorine-fluorodeoxyglucose PET-CT findings in a case of rarely seen metastatic adult extrarenal Wilms' tumor of retroperitoneum presenting as lower limb edema.

Authors:  Vankadari Kousik; Bharat A Vaswani; Milap Milap; Sai Ram
Journal:  World J Nucl Med       Date:  2021-09-22
  3 in total

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