[Arthrogryposis multiplex congenita of the upper extremity].

This article is a comprehensive review on arthrogryposis multiplex congenita of the upper extremity. The introduction contains information on definition, etiology, pathogenesis, differential diagnosis and manifestations outside the upper extremity. The main section focuses on the upper limb and expands on epidemiology, patterns of deformity, their natural evolution, on related functional problems, and general principles of treatment. Finally, the various regional deformities are presented and guidelines are given for conservative or operative treatment.