Literature DB >> 8227584

Hallervorden-Spatz disease with bilateral involvement of globus pallidus and substantia nigra: MR demonstration.

L Porter-Grenn1, R Silbergleit, B A Mehta.   

Abstract

Hallervorden-Spatz disease presents with relentless mental and physical deterioration. Pathologically there is abnormal iron deposition in the globi pallidi, substantia nigra, and red nuclei. A spectrum of abnormal basal ganglia signal intensities have been described on MRI. A pediatric case with low signal intensity in the globi pallidi and substantia nigra is presented.

Entities:  

Mesh:

Year:  1993        PMID: 8227584     DOI: 10.1097/00004728-199311000-00019

Source DB:  PubMed          Journal:  J Comput Assist Tomogr        ISSN: 0363-8715            Impact factor:   1.826


  2 in total

1.  Neuro-ophthalmologic and electroretinographic findings in pantothenate kinase-associated neurodegeneration (formerly Hallervorden-Spatz syndrome).

Authors:  Robert A Egan; Richard G Weleber; Penelope Hogarth; Allison Gregory; Jason Coryell; Shawn K Westaway; Jane Gitschier; Soma Das; Susan J Hayflick
Journal:  Am J Ophthalmol       Date:  2005-08       Impact factor: 5.258

2.  Age-related pathology and biosenescent markers in captive rhesus macaques.

Authors:  H Uno
Journal:  Age (Omaha)       Date:  1997-01
  2 in total

北京卡尤迪生物科技股份有限公司 © 2022-2023.