Literature DB >> 8216523

Multiple trauma in the achondroplastic dwarf: an emergency medicine physician perspective case report and literature review.

D M Dvorak1, R A Rusnak, J J Morcos.   

Abstract

Although uncommon, the achondroplastic dwarf (AD) may become the victim of multiple trauma, presenting special challenges for the emergency department (ED) physician. Traditional management of airway, breathing, circulation, and neurological disability is altered by the unique anatomic features of achondroplasia. Despite facial abnormalities observed in the AD, orotracheal and nasotracheal intubation are usually accomplished without particular difficulty; however, abnormalities of the base of the skull and cervical spine make hyperextension of the neck especially hazardous in these patients. The lungs are functionally normal, although vital capacity is decreased and thoracic case abnormalities and abdominal obesity impair lung expansion. Vascular access in the AD is difficult. Peripheral access is difficult because of excessive subcutaneous fat, whereas central venous access is complicated by neck, chest wall, and spinal abnormalities that obscure commonly used anatomic landmarks. Major neurological syndromes observed in ADs are hydrocephalus, cervical medullary compression, and thoracolumbar stenosis. The ED physician should recognize these syndromes, their potential to produce neurological disability, and their unique implications for trauma.

Entities:  

Mesh:

Year:  1993        PMID: 8216523     DOI: 10.1016/0735-6757(93)90174-a

Source DB:  PubMed          Journal:  Am J Emerg Med        ISSN: 0735-6757            Impact factor:   2.469


  1 in total

Review 1.  Acute upper airway obstruction and emergency front of neck access in an achondroplastic patient.

Authors:  Craig James McCaffer; Catriona Douglas; Matthew H Wickham; Gerard L Picozzi
Journal:  BMJ Case Rep       Date:  2015-03-31
  1 in total

北京卡尤迪生物科技股份有限公司 © 2022-2023.