Pulmonary artery aneurysm due to severe congenital pulmonic stenosis. Case report and literature review.

Although dilatation of the pulmonary artery (PA) is characteristic of pulmonic valve stenosis (PVS), the occurrence of a PA aneurysm in association with PVS is very rare. The authors describe a patient with severe, dome-shaped PVS who developed a 6.5 cm pulmonary trunk aneurysm. Long-term follow-up after surgical valvotomy demonstrated that the size of the aneurysm remained unchanged. Pertinent literature and implications on the natural history and management of these aneurysms are discussed.