Literature DB >> 8016804

Diffuse pulmonary fibrosis and the Hermansky-Pudlak syndrome: clinical course and postmortem findings.

S P Reynolds1, B H Davies, A R Gibbs.   

Abstract

The Hermansky-Pudlak syndrome consists of albinism, platelet function defect, pigment laden macrophases and, on occasions, pulmonary fibrosis. The clinical course and postmortem findings of a patient with pulmonary fibrosis which mimicked cryptogenic fibrosing alveolitis are reported. Histological examination revealed a chronic inflammatory infiltrate of pigment laden microphages.

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Year:  1994        PMID： 8016804      PMCID： PMC474969          DOI： 10.1136/thx.49.6.617

Source DB:  PubMed          Journal:  Thorax        ISSN： 0040-6376            Impact factor:   9.139


  8 in total

1.  VASCULAR PSEUDOHEMOPHILIA ASSOCIATED WITH CEROID PIGMENTOPHAGIA IN ALBINOS.

Authors:  B BEDNAR; F HERMANSKY; Z LOJDA
Journal:  Am J Pathol       Date:  1964-08       Impact factor: 4.307

2.  Albinism associated with hemorrhagic diathesis and unusual pigmented reticular cells in the bone marrow: report of two cases with histochemical studies.

Authors:  F HERMANSKY; P PUDLAK
Journal:  Blood       Date:  1959-02       Impact factor: 22.113

3.  Familial pulmonary fibrosis associated with oculocutaneous albinism and platelet function defect. A new syndrome.

Authors:  B H Davies; E G Tuddenham
Journal:  Q J Med       Date:  1976-04

4.  Hermansky-Pudlak syndrome with special reference to lysosomal dysfunction. A case report and review of the literature.

Authors:  A Takahashi; T Yokoyama
Journal:  Virchows Arch A Pathol Anat Histopathol       Date:  1984

5.  Hermansky-Pudlak syndrome with granulomatous colitis.

Authors:  R A Schinella; M A Greco; B L Cobert; L W Denmark; R P Cox
Journal:  Ann Intern Med       Date:  1980-01       Impact factor: 25.391

6.  Hermansky-Pudlak syndrome. Pulmonary manifestations of a ceroid storage disorder.

Authors:  S M Garay; J E Gardella; E P Fazzini; R M Goldring
Journal:  Am J Med       Date:  1979-05       Impact factor: 4.965

7.  Hermansky-pudlak syndrome and interstitial lung disease: report of a case with lavage findings.

Authors:  D A White; G J Smith; J A Cooper; M Glickstein; J A Rankin
Journal:  Am Rev Respir Dis       Date:  1984-07

Review 8.  The Hermansky-Pudlak syndrome. Report of three cases and review of pathophysiology and management considerations.

Authors:  R A DePinho; K L Kaplan
Journal:  Medicine (Baltimore)       Date:  1985-05       Impact factor: 1.889
  8 in total
  2 in total

1.  Diffuse pulmonary fibrosis and Hermansky-Pudlak syndrome.

Authors:  W Wöckel; J Sültz
Journal:  Thorax       Date:  1995-05       Impact factor: 9.139

2.  Epithelial stress and apoptosis underlie Hermansky-Pudlak syndrome-associated interstitial pneumonia.

Authors:  Poornima Mahavadi; Martina Korfei; Ingrid Henneke; Gerhard Liebisch; Gerd Schmitz; Bernadette R Gochuico; Philipp Markart; Saverio Bellusci; Werner Seeger; Clemens Ruppert; Andreas Guenther
Journal:  Am J Respir Crit Care Med       Date:  2010-04-08       Impact factor: 21.405
  2 in total

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