Literature DB >> 7997556

Trisomy 13 syndrome: prenatal US findings in a review of 33 cases.

C D Lehman1, D A Nyberg, T C Winter, R P Kapur, R G Resta, D A Luthy.   

Abstract

PURPOSE: To determine the type and prevalence of prenatal ultrasound (US) findings in fetuses with trisomy 13.
MATERIALS AND METHODS: Prenatal US findings in 33 consecutive fetuses with trisomy 13 and in 200 karyotypically normal fetuses were reviewed and compared.
RESULTS: One or more abnormalities were found in 30 fetuses (91%). Major anomalies detected by means of US included holoprosencephaly (13 [39%]) or other central nervous system anomalies (19 [58%]), facial anomalies (15 [48%]), and renal (11 [33%]) and cardiac (16 [48%]) defects. Growth retardation was also present in 16 (48%). Echogenic chordae tendineae were seen in 10 (30%), which includes seven (39%) of 18 fetuses examined before 20 menstrual weeks (compared with four [2%] of 200 fetuses in the reference group [P < .001]). Other findings not generally associated with trisomy 13 but present in this series included a large cisterna magna (six [18%]), mild cerebral ventricular dilatation (three [9%]), nuchal thickening or cystic hygroma (seven [21%]), and a hypoplastic left side of the heart (seven [21%]).
CONCLUSION: Prenatal US can help detect one or more anomalies in most fetuses with trisomy 13; thus, US finding can indicate whether karyotype should be tested.

Entities:  

Mesh:

Year:  1995        PMID: 7997556     DOI: 10.1148/radiology.194.1.7997556

Source DB:  PubMed          Journal:  Radiology        ISSN: 0033-8419            Impact factor:   11.105


  13 in total

1.  Neuroradiological findings of trisomy 13 in a rare long-term survivor.

Authors:  Ryan D Goff; Bruno P Soares
Journal:  Neuroradiol J       Date:  2017-02-14

2.  Duplication of the ZIC2 gene is not associated with holoprosencephaly.

Authors:  Vaidehi Jobanputra; Alanna Burke; Anyane-Yeboa Kwame; Anita Shanmugham; Maryam Shirazi; Stephen Brown; Peter E Warburton; Brynn Levy; Dorothy Warburton
Journal:  Am J Med Genet A       Date:  2011-11-21       Impact factor: 2.802

3.  Syndromes associated with holoprosencephaly.

Authors:  Paul Kruszka; Maximilian Muenke
Journal:  Am J Med Genet C Semin Med Genet       Date:  2018-05-17       Impact factor: 3.908

Review 4.  The role of ultrasound in the diagnosis of fetal genetic syndromes.

Authors:  Shayna N Conner; Ryan E Longman; Alison G Cahill
Journal:  Best Pract Res Clin Obstet Gynaecol       Date:  2014-01-28       Impact factor: 5.237

Review 5.  Holoprosencephaly due to numeric chromosome abnormalities.

Authors:  Benjamin D Solomon; Kenneth N Rosenbaum; Jeanne M Meck; Maximilian Muenke
Journal:  Am J Med Genet C Semin Med Genet       Date:  2010-02-15       Impact factor: 3.908

6.  Application of Single Nucleotide Polymorphism Microarray in Prenatal Diagnosis of Fetuses with Central Nervous System Abnormalities.

Authors:  Xiaorui Xie; Xiaoqing Wu; Linjuan Su; Meiying Cai; Ying Li; Hailong Huang; Liangpu Xu
Journal:  Int J Gen Med       Date:  2021-08-06

7.  Patterns of congenital anomalies among individuals with trisomy 13 in Texas.

Authors:  Diego Diaz; Renata H Benjamin; Maria Luisa Navarro Sanchez; Laura E Mitchell; Peter H Langlois; Mark A Canfield; Han Chen; Angela E Scheuerle; Christian P Schaaf; Daryl A Scott; Hope Northrup; Joseph W Ray; Scott D McLean; Michael D Swartz; Katherine L Ludorf; Philip J Lupo; A J Agopian
Journal:  Am J Med Genet A       Date:  2021-03-22       Impact factor: 2.578

Review 8.  Trisomy 13, 18, 21, Triploidy and Turner syndrome: the 5T's. Look at the hands.

Authors:  G Witters; J Van Robays; C Willekes; A Coumans; H Peeters; W Gyselaers; J P Fryns
Journal:  Facts Views Vis Obgyn       Date:  2011

9.  Holoprosencephaly and klinefelter syndrome.

Authors:  Shahin Abdollahifakhim; Ebrahim Sakhinia; Mehrnoosh Mousaviagdas
Journal:  Iran J Pediatr       Date:  2014-04       Impact factor: 0.364

10.  An ethnic predilection for fetal echogenic intracardiac focus identified during targeted midtrimester ultrasound examination: A retrospective review.

Authors:  Andrei Rebarber; Kenneth A Levey; Edmund Funai; Susan Monda; Michael Paidas
Journal:  BMC Pregnancy Childbirth       Date:  2004-06-25       Impact factor: 3.007

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