Literature DB >> 7797016

Screening blood donors for hereditary hemochromatosis: decision analysis model based on a 30-year database.

P C Adams1, J C Gregor, A E Kertesz, L S Valberg.   

Abstract

BACKGROUND & AIMS: The high prevalence, morbidity, premature death, and benefit of early diagnosis and treatment make hemochromatosis a prime target for screening in the white population. Decision analysis techniques were used to compare the outcome, utility, and incremental cost savings of a plan to screen voluntary blood donors for hemochromatosis.
METHODS: The screening strategy includes sequential testing of serum unsaturated iron-binding capacity, serum transferrin saturation, serum ferritin, and either hepatic iron index or venesections to measure exchangeable body iron. Estimates of prevalence, asymptomatic intervals, probabilities of life-threatening clinical complications, symptom-specific life expectancy, and sensitivity and specificity of screening tests are based on our database of 170 hemochromatosis homozygotes and the published literature.
RESULTS: The screening strategy led to an incremental increase in utility of 0.84 quality-adjusted life days with an incremental cost savings of $3.19 per blood donor screened. When the potential of identifying asymptomatic homozygous siblings was included, these values increased to 1.18 quality-adjusted life days and $12.57 per person screened. Screening remained a dominant strategy given a prevalence of hemochromatosis of > 0.0026 or an initial screening test cost of < $8.
CONCLUSIONS: Screening blood donors for hemochromatosis has the potential to improve overall societal health status and decrease third-party payer health care costs over the long-term.

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Year:  1995        PMID: 7797016     DOI: 10.1016/0016-5085(95)90283-x

Source DB:  PubMed          Journal:  Gastroenterology        ISSN: 0016-5085            Impact factor:   22.682


  21 in total

1.  Population screening for haemochromatosis.

Authors:  P C Adams
Journal:  Gut       Date:  2000-03       Impact factor: 23.059

2.  Hereditary haemochromatosis should be more widely known about.

Authors:  W Rosenberg; M Howell; P Roderick; D Eccles; I Day
Journal:  BMJ       Date:  1999-05-29

3.  Global prevalence of putative haemochromatosis mutations.

Authors:  A T Merryweather-Clarke; J J Pointon; J D Shearman; K J Robson
Journal:  J Med Genet       Date:  1997-04       Impact factor: 6.318

4.  Predictive value of family history in diagnosis of hereditary hemochromatosis.

Authors:  N Assy; P C Adams
Journal:  Dig Dis Sci       Date:  1997-06       Impact factor: 3.199

5.  46,XX, inv(6)(p21.1p23) in a pedigree with hereditary haemochromatosis.

Authors:  C P Venditti; N K Seese; G S Gerhard; A E Ten Elshof; K A Chorney; P N Mowrey; P G Lacey; J H Knoll; M J Chorney
Journal:  J Med Genet       Date:  1997-01       Impact factor: 6.318

6.  A simple genetic test identifies 90% of UK patients with haemochromatosis. The UK Haemochromatosis Consortium.

Authors: 
Journal:  Gut       Date:  1997-12       Impact factor: 23.059

7.  Clinical penetrance of C282Y homozygous HFE haemochromatosis.

Authors:  Enrico Rossi; Gary P Jeffrey
Journal:  Clin Biochem Rev       Date:  2004-08

8.  The significance of haemochromatosis gene mutations in the general population: implications for screening.

Authors:  M J Burt; P M George; J D Upton; J A Collett; C M Frampton; T M Chapman; T A Walmsley; B A Chapman
Journal:  Gut       Date:  1998-12       Impact factor: 23.059

Review 9.  Is genetic screening for hemochromatosis worthwhile?

Authors:  Omer T Njajou; Behrooz Z Alizadeh; Cornelia M van Duijn
Journal:  Eur J Epidemiol       Date:  2004       Impact factor: 8.082

10.  Screening for hemochromatosis in Turkey.

Authors:  Hakan Bozkaya; Mehmet Bektas; Olga Metin; Ozlem Erkan; Dicle Ibrahimoglu; Klara Dalva; Filiz Akbiyik; Selim Gurel; Abdurrahman Mithat Bozdayi; Cemal Akay; Cihan Yurdaydin; Onder Aslan; Ozden Uzunalimoglu
Journal:  Dig Dis Sci       Date:  2004-03       Impact factor: 3.199

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