Literature DB >> 7785020

Bronchiectasis and homozygous (P1ZZ) alpha 1-antitrypsin deficiency in a young man.

W Rodriguez-Cintron1, K Guntupalli, A E Fraire.   

Abstract

Pulmonary complications of alpha 1-antitrypsin deficiency are most commonly manifested by panlobular emphysema. This report describes histologically proven bronchiectasis in a 21 year old man with massive haemoptysis and homozygous deficiency of alpha 1-antitrypsin. Neither panlobular emphysema nor cirrhosis of the liver were present. Bronchiectasis must be considered part of the spectrum of the pulmonary pathology that may be encountered in individuals with alpha 1-antitrypsin deficiency.

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Year:  1995        PMID： 7785020      PMCID： PMC474302          DOI： 10.1136/thx.50.4.424

Source DB:  PubMed          Journal:  Thorax        ISSN： 0040-6376            Impact factor:   9.139


  9 in total

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Journal:  Chest       Date:  1975-02       Impact factor: 9.410

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Journal:  Acta Med Scand       Date:  1978

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Journal:  Chest       Date:  1977-04       Impact factor: 9.410

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Journal:  Clin Chest Med       Date:  1988-12       Impact factor: 2.878

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Journal:  Br J Dis Chest       Date:  1983-01

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  9 in total
  2 in total

1.  Bronchiectasis and homozygous (P1ZZ) alpha 1-antitrypsin deficiency.

Authors:  F Al-Kassimi
Journal:  Thorax       Date:  1996-02       Impact factor: 9.139

2.  A preliminary assessment of alpha-1 antitrypsin S and Z deficiency allele frequencies in common variable immunodeficiency patients with and without bronchiectasis.

Authors:  M E Sansom; B L Ferry; Z P M C Sherrell; H M Chapel
Journal:  Clin Exp Immunol       Date:  2002-12       Impact factor: 4.330
  2 in total

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