Multiple arteriovenous malformations in a man with a connective tissue disorder.

Multiple arteriovenous malformations in patients with connective tissue disorders are not reported. We describe a man with cutaneous, ligament/articular and vascular features suggestive of a connective tissue disorder and who also has multiple arteriovenous malformations resulting in a high output circulatory state. Chest pain due to arteriovenous malformations originating from subclavian vessels has caused considerable morbidity.