Double-outlet right ventricle. A collective review with a surgical viewpoint.

Double-outlet right ventricle (DORV) should be classified according to its various subsets. Van Praagh's symbolic terminology provides an appropriate mechanism for doing that. Each of these subsets is described in terms of its pathology, clinical characteristics, cardiac catheterization findings, and operative repair. The operative repair for each is different. The presence or absence of continuity between the semilunar and atrioventricular valves is unimportant from the standpoint of operation and should not be a criterion for classification.