Literature DB >> 7469447

Transfusion therapy in a patient with erythropoietic protoporphyria.

M A Bechtel, S J Bertolone, S J Hodge.   

Abstract

An 8-year-old boy with erythropoietic protoporphyria had a marked decrease in photosensitivity symptoms after several transfusions with washed, packed RBCs. The reduction in photosensitivity was associated with a decline in free erythrocyte protoporphyrin levels.

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Year:  1981        PMID: 7469447

Source DB:  PubMed          Journal:  Arch Dermatol        ISSN: 0003-987X


  4 in total

Review 1.  Liver disease in erythropoietic protoporphyria: insights and implications for management.

Authors:  A V Anstey; R J Hift
Journal:  Postgrad Med J       Date:  2007-12       Impact factor: 2.401

Review 2.  Liver disease in erythropoietic protoporphyria: insights and implications for management.

Authors:  A V Anstey; R J Hift
Journal:  Gut       Date:  2007-03-14       Impact factor: 23.059

3.  Protoporphyrin hepatopathy. Effects of cholic acid ingestion in murine griseofulvin-induced protoporphyria.

Authors:  M B Poh-Fitzpatrick; J A Sklar; C Goldsman; J H Lefkowitch
Journal:  J Clin Invest       Date:  1983-10       Impact factor: 14.808

Review 4.  Iron, Heme Synthesis and Erythropoietic Porphyrias: A Complex Interplay.

Authors:  Antoine Poli; Caroline Schmitt; Boualem Moulouel; Arienne Mirmiran; Hervé Puy; Thibaud Lefèbvre; Laurent Gouya
Journal:  Metabolites       Date:  2021-11-23
  4 in total

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