Literature DB >> 7449178

Sotos syndrome with intestinal polyposis and pigmentary changes of the genitalia.

R H Ruvalcaba, S Myhre, D W Smith.   

Abstract

We report two adult males with the Sotos syndrome, who also presented intestinal polyposis and pigmentary spotting of the shaft and glans penis. We propose that patients with the Sotos syndrome may develop hamartoneoplastic disease and we urge clinicians to consider this possibility in those patients.

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Mesh：

Year:  1980        PMID： 7449178     DOI： 10.1111/j.1399-0004.1980.tb01785.x

Source DB:  PubMed          Journal:  Clin Genet        ISSN： 0009-9163            Impact factor:   4.438


  18 in total

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