Single system ectopic ureteroceles with anomalies of the heart, testis and vas deferens.

We report a series of 7 children with single system ectopic ureteroceles. Our study included 6 boys, unlike the more common duplicated system ectopic ureterocele, that occurs 4 to 6 times more often in female patients. The presenting symptoms or signs were related to infection or obstruction in only 2 of our 7 patients. An ipsilateral non-functioning hypoplastic dysplastic kidney was present in 5 children (71%). Of the 7 children 4 had major congenital cardiac anomalies. Three boys had abdominal testes, including 2 with bilateral non-union of the vas deferens, 1 of whom represents the first reported case of bilateral atresia of the vas deferens with abdominal testes.