Interrupted aortic arch type A associated with congenitally corrected transposition of great arteries and ventricular septal defect. Successful direct aortic anastomosis and pulmonary artery banding in an infant.

A case is described of congenitally corrected transposition of the great arteries (atrioventricular discordance, ventriculoarterial discordance) with interrupted aortic arch, a previously unreported association. Aortic continuity was achieved by direct surgical anastomosis. Pulmonary artery banding was subsequently necessary, because of heart failure associated with a large ventricular septal defect. A possible pathogenetic mechanism is suggested.