Literature DB >> 7265046

[Intra-osseus hemorrhagic lesions in congenital afibrinogenemia. A new case (author's transl)].

J C Zenny, A Chevrot, Y Sultan, D Godefroy, P Horreard, G Pallardy.   

Abstract

Congenital afibrinemia is a rare disease, transmitted by an autosomal recessive mode, and due to deficient fibrinogen. Osseous involvement is exceptional, since only 2 cases have been reported. We describe a third case. The roentgenographic features are well limited radiolucent lesions, arising in the medullary space, and slightly expanding. These lesions are related to fibrous cysts, resulting from intraosseous hemorrhages. Spontaneous resolution may occur: the absence of fibrin deposits and blood clot probably favours resorption.

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Year:  1981        PMID: 7265046

Source DB:  PubMed          Journal:  J Radiol        ISSN: 0221-0363


  1 in total

1.  A Rare Complication of Congenital Afibrinogenemia: Bone Cysts.

Authors:  Ali Fettah; Dilek Gürlek Gökçebay; Vildan Çulha; Neşe Yaralı; Bahattin Tunç; Namık Özbek
Journal:  Turk J Haematol       Date:  2016-04-18       Impact factor: 1.831

  1 in total

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