Single ventricle with aortic outflow obstruction: operative repair by creation of double outlet to the aorta and application of the Fontan principle.

A new operation is described which allows the Fontan procedure to be used in patients having single ventricle accompanied by aortic outflow obstruction. Connection of the proximal pulmonary artery and valve to the aorta via a tubular prosthesis provides a second outlet of the ventricle to the aorta in order to effectively bypass subaortic obstruction. Anastomosis of a distal pulmonary artery to the right atrium and closure of the atrial septum by patch (Fontan procedure) complete the establishment of unrestricted pulmonary and systemic circulations in series.