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Literature DB >> 7172963

D-penicillamine in Wilson's disease presenting as acute liver failure with hemolysis.

W Vielhauer, V Eckardt, K H Holtermüller, J B Lüth, B Schulte, W Prellwitz, W Sonntag.

Abstract

Wilson's disease in a young woman presenting with an acute course is described. The clinical manifestations were fulminant hepatic failure associated with marked intravascular hemolysis. Immediate D-penicillamine and high-dose steroid therapy did not influence the course of the disease. Necropsy revealed an increased hepatic copper content and cirrhosis with extensive necrosis of the liver.

Entities: Chemical Disease Species

Mesh：

Substances：

Year: 1982 PMID： 7172963 DOI： 10.1007/bf01391452

Source DB: PubMed Journal: Dig Dis Sci ISSN： 0163-2116 Impact factor: 3.199

25 in total

1. The anemia of liver disease: observations on its mechanism.

Authors: J H JANDL
Journal: J Clin Invest Date: 1955-03 Impact factor: 14.808

2. The liver in juvenile Wilson's disease.

Authors: M SILVERBERG; S S GELLIS
Journal: Pediatrics Date: 1962-09 Impact factor: 7.124

3. Penicillamine, a new oral therapy for Wilson's disease.

Authors: J M WALSHE
Journal: Am J Med Date: 1956-10 Impact factor: 4.965

4. Histochemical localization of copper with rubeanic acid.

Authors: L L UZMAN
Journal: Lab Invest Date: 1956 May-Jun Impact factor: 5.662

5. Chronic hepatitis as a first manifestation of Wilson's disease.

Authors: I Sternlieb; I H Scheinberg
Journal: Ann Intern Med Date: 1972-01 Impact factor: 25.391

6. Long-term therapy of Wilson's disease.

Authors: A Deiss; R E Lynch; G R Lee; G E Cartwright
Journal: Ann Intern Med Date: 1971-07 Impact factor: 25.391

7. Hemolytic anemia in Wilson's disease.

Authors: N McIntyre; H M Clink; A J Levi; J N Cumings; S Sherlock
Journal: N Engl J Med Date: 1967-02-23 Impact factor: 91.245

8. Hepatolenticular degeneration (Wilson's disease) as a form of idiopathic cirrhosis.

Authors: T C CHALMERS; F L IBER; L L UZMAN
Journal: N Engl J Med Date: 1957-02-07 Impact factor: 91.245

9. Acute case of Wilson's disease (hepatolenticular degeneration).

Authors: N R LAWRIE; R A CARTER
Journal: Lancet Date: 1958-06-21 Impact factor: 79.321

10. Progressive lenticular degeneration: a familial nervous disease associated with cirrhosis of the liver, by S. A. Kinnier Wilson, (From the National Hospital, and the Laboratory of the National Hospital, Queen Square, London) Brain 1912: 34; 295-509.

Authors: Alastair Compston
Journal: Brain Date: 2009-08 Impact factor: 13.501

1 in total

1. Antemortem diagnosis and short-term survival of a patient with Wilson's disease presenting as fulminant hepatic failure.

Authors: A J McCullough; R H Wiesner; C R Fleming; E R Dickson
Journal: Dig Dis Sci Date: 1984-09 Impact factor: 3.199

1 in total